Late-onset hereditary ataxia with global thermoanalgesia and absence of fungiform papillae on the tongue in a Japanese family

Brain

Volumn 119, Issue 3, 1996, Pages 1011-1021

  Fukutake, T ^a   Kita, K ^a   Sakakibara, R ^a   Takagi, K ^a   Tokumaru, Y ^a   Kojima, S ^a   Hattori, T ^a   Hirayama, K ^a  

^a CHIBA UNIVERSITY   (Japan)

Author keywords

Familial dysautonomia (Riley Day syndrome); Fungiform papillae on the tongue (or ageusia); Hereditary ataxia; Hereditary sensory and autonomic neuropathy; Thermoanalgesia

Indexed keywords

ADULT; AGED; AGEUSIA; ANALGESIA; ARTICLE; AUTONOMIC NEUROPATHY; BLOOD PRESSURE REGULATION; BRAIN STEM; BRAIN VENTRICLE; CASE REPORT; CEREBELLUM; CHOLINERGIC SYSTEM; CONSTIPATION; CORPUS CALLOSUM; DIARRHEA; DYSPHAGIA; HEMIFACIAL ATROPHY; HEREDITARY ATAXIA; HUMAN; HUMAN TISSUE; LACRIMAL FLUID; MALE; MYELINATED NERVE; NERVE BIOPSY; NERVE FIBER DEGENERATION; ONSET AGE; PARESIS; PERCEPTION DEAFNESS; PRIORITY JOURNAL; SPINOCEREBELLAR DEGENERATION; SURAL NERVE; TASTE BUD; TONGUE; URINARY DYSFUNCTION; VASOMOTOR REFLEX;

BIOPSY; BRAIN; CARDIOVASCULAR SYSTEM; DEGLUTITION; DYSAUTONOMIA, FAMILIAL; ELECTROENCEPHALOGRAPHY; EVOKED POTENTIALS, AUDITORY, BRAIN STEM; EVOKED POTENTIALS, SOMATOSENSORY; HEAT; HEREDITARY SENSORY AND AUTONOMIC NEUROPATHIES; HISTAMINE AGENTS; HUMANS; JAPAN; MALE; MIDDLE AGED; NEURAL CONDUCTION; PAIN MEASUREMENT; PEDIGREE; PUPIL; SALIVATION; SPINAL CORD; SPINOCEREBELLAR DEGENERATIONS; SURAL NERVE; SWEATING; TASTE BUDS; TEARS; TOMOGRAPHY, X-RAY COMPUTED; TONGUE; URINARY BLADDER;

EID: 0030012898     PISSN: 00068950     EISSN: None     Source Type: Journal    
DOI: 10.1093/brain/119.3.1011     Document Type: Article

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