Electrophoretic separation of multiprotein complexes from blood platelets and cell lines: Technique for the analysis of diseases with defects in oxidative phosphorylation

Electrophoresis

Volumn 17, Issue 4, 1996, Pages 709-714

  Schägger, Hermann ^a   Bentlage, Herman ^b   Ruitenbeek, Wim ^b   Pfeiffer, Kathy ^a   Rotter, Stefan ^a   Rother, Christof ^a   Böttcher Purkl, Andrea ^a   Lodemann, Edgar ^a  

^a UNIVERSITY HOSPITAL FRANKFURT   (Germany)

^b RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

Author keywords

Blue native electrophoresis; Complex; Integrins; Mitochondrial encephalomyopathy; Pearson syndrome; Platelet membrane glycoprotein

Indexed keywords

CELL CULTURE; DEFECTS; GLYCOPROTEINS; PHOSPHORYLATION; PROTEINS; SODIUM DODECYL SULFATE; SULFUR COMPOUNDS; TISSUE;

BLUE-NATIVE ELECTROPHORESIS; COMPLEX; CULTURED CELL; INTEGRINS; MITOCHONDRIAL ENCEPHALOMYOPATHY; OXIDATIVE PHOSPHORYLATION; PEARSON SYNDROME; PLATELET MEMBRANE GLYCOPROTEIN; PLATELET MEMBRANES; PROTEIN SUBUNITS;

ELECTROPHORESIS;

ANIMAL CELL; ARTICLE; AUTOPSY; BIOPSY; BLEEDING DISORDER; CELL CULTURE; CELL LINE; CELL STRAIN L 929; CONTROLLED STUDY; ENCEPHALOMYOPATHY; ENZYME ANALYSIS; GLANZMANN DISEASE; HUMAN; HUMAN CELL; HUMAN TISSUE; METABOLIC DISORDER; NONHUMAN; OXIDATIVE PHOSPHORYLATION; POLYACRYLAMIDE GEL ELECTROPHORESIS; PROTEIN ANALYSIS; SILVER STAINING; SKIN FIBROBLAST; TECHNIQUE; THROMBOCYTE;

EID: 0029980819     PISSN: 01730835     EISSN: None     Source Type: Journal    
DOI: 10.1002/elps.1150170415     Document Type: Article

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