메뉴 건너뛰기




Volumn 57, Issue 1, 1996, Pages 31-36

Chronic sodium benzoate therapy in children with inborn errors of urea synthesis: Effect on carnitine metabolism and ammonia nitrogen removal

Author keywords

[No Author keywords available]

Indexed keywords

BENZOIC ACID; CARNITINE;

EID: 0029974447     PISSN: 10773150     EISSN: None     Source Type: Journal    
DOI: 10.1006/bmme.1996.0006     Document Type: Article
Times cited : (15)

References (31)
  • 1
    • 0001878491 scopus 로고
    • Urea cycle enzymes
    • New York: McGraw-Hill, Scriver CR, Beaudet AL, Sly WS, Valle D, (Eds.)
    • Brusilow SW, Horwich AL. Urea cycle enzymes. In New York: McGraw-Hill, "The Metabolic Basis of Inherited Disease" Scriver CR, Beaudet AL, Sly WS, Valle D, (Eds.). 1989, pp 629-663.
    • (1989) The Metabolic Basis of Inherited Disease , pp. 629-663
    • Brusilow, S.W.1    Horwich, A.L.2
  • 2
    • 0016062676 scopus 로고
    • Ornithinemia, hyperammonemia and homocitrullinuria: A disease associated with mental retardation and possibly caused by defective mitochondrial transport
    • Fell V, Pollitt RJ, Sampson GA, Wright T. Ornithinemia, hyperammonemia and homocitrullinuria: A disease associated with mental retardation and possibly caused by defective mitochondrial transport. Am J Dis Child 127:752-756, 1974.
    • (1974) Am J Dis Child , vol.127 , pp. 752-756
    • Fell, V.1    Pollitt, R.J.2    Sampson, G.A.3    Wright, T.4
  • 3
    • 0021231177 scopus 로고
    • Treatment of congenital hyperammonemias
    • Bachmann C. Treatment of congenital hyperammonemias. Enzyme 32:56-64, 1984.
    • (1984) Enzyme , vol.32 , pp. 56-64
    • Bachmann, C.1
  • 4
    • 0020057470 scopus 로고
    • Treatment of inborn errors of urea synthesis
    • Batshaw ML, Brusilow S, Waber L et al. Treatment of inborn errors of urea synthesis. N Engl J Med 306:1387-1392, 1982.
    • (1982) N Engl J Med , vol.306 , pp. 1387-1392
    • Batshaw, M.L.1    Brusilow, S.2    Waber, L.3
  • 5
    • 0022415171 scopus 로고
    • Chronic benzoate therapy in a boy with partial ornithine transcarbamylase deficiency
    • Letarte J, Qureshi IA, Quellet R, Godard M. Chronic benzoate therapy in a boy with partial ornithine transcarbamylase deficiency. J Pediatr 106:794-797, 1985.
    • (1985) J Pediatr , vol.106 , pp. 794-797
    • Letarte, J.1    Qureshi, I.A.2    Quellet, R.3    Godard, M.4
  • 6
    • 0020684054 scopus 로고
    • Effect of long-term administration of sodium benzoate to a patient with partial ornithine carbamoyl transferase deficiency
    • Takeda E, Kuroda Y, Toshima K, Watanabe T, Naito E, Miyao M. Effect of long-term administration of sodium benzoate to a patient with partial ornithine carbamoyl transferase deficiency. Clin Pediatr 22:206-208, 1983.
    • (1983) Clin Pediatr , vol.22 , pp. 206-208
    • Takeda, E.1    Kuroda, Y.2    Toshima, K.3    Watanabe, T.4    Naito, E.5    Miyao, M.6
  • 7
    • 34250243686 scopus 로고
    • Evidence of lack of toxicity of sodium phenylacetate and sodium benzoate in treating urea cycle enzymopathies
    • Batshaw ML, Brusilow SW. Evidence of lack of toxicity of sodium phenylacetate and sodium benzoate in treating urea cycle enzymopathies. J Inherit Metab Dis 4:231, 1981.
    • (1981) J Inherit Metab Dis , vol.4 , pp. 231
    • Batshaw, M.L.1    Brusilow, S.W.2
  • 9
    • 0006276946 scopus 로고
    • Studies in the synthesis of hippuric acid in the animal organism
    • Lewis HB. Studies in the synthesis of hippuric acid in the animal organism. J Biol Chem 18:225-231, 1914.
    • (1914) J Biol Chem , vol.18 , pp. 225-231
    • Lewis, H.B.1
  • 10
    • 0001129813 scopus 로고
    • The clinical application of the hippuric acid and the prothrombin tests
    • Quick AJ. The clinical application of the hippuric acid and the prothrombin tests. Am J Clin Pathol 10:222-233, 1940.
    • (1940) Am J Clin Pathol , vol.10 , pp. 222-233
    • Quick, A.J.1
  • 11
    • 0343977708 scopus 로고
    • The chemical estimation of acyl glucuronides and its application to studies on the metabolism of benzoate and salicylate in man
    • Schachter D. The chemical estimation of acyl glucuronides and its application to studies on the metabolism of benzoate and salicylate in man. J Clin Invest 36:297-302, 1957.
    • (1957) J Clin Invest , vol.36 , pp. 297-302
    • Schachter, D.1
  • 12
    • 0024583295 scopus 로고
    • Excretion of hippuric acid during sodium benzoate therapy in patients with hyperglycinaemia or hyperammonaemia
    • Barshop BA, Breuer J, Holm J, Leslie J, Nyhan L. Excretion of hippuric acid during sodium benzoate therapy in patients with hyperglycinaemia or hyperammonaemia. J Inherit Metab Dis 12:72-79, 1989.
    • (1989) J Inherit Metab Dis , vol.12 , pp. 72-79
    • Barshop, B.A.1    Breuer, J.2    Holm, J.3    Leslie, J.4    Nyhan, L.5
  • 13
    • 0021327264 scopus 로고
    • Treatment of hyperargininemia with sodium benzoate and arginine-restricted diet
    • Qureshi IA, Letarte J, Quellet R, Batshaw ML, Brusilow S. Treatment of hyperargininemia with sodium benzoate and arginine-restricted diet. J Pediatr 104:473-476, 1984.
    • (1984) J Pediatr , vol.104 , pp. 473-476
    • Qureshi, I.A.1    Letarte, J.2    Quellet, R.3    Batshaw, M.L.4    Brusilow, S.5
  • 14
    • 8044224506 scopus 로고
    • The formation of hippuric acid: The influence of benzoate administration on tissue glycine levels
    • Simkim JL, White K. The formation of hippuric acid: the influence of benzoate administration on tissue glycine levels. Biochem J 65:574-582, 1957.
    • (1957) Biochem J , vol.65 , pp. 574-582
    • Simkim, J.L.1    White, K.2
  • 15
    • 0025734484 scopus 로고
    • Carnitine deficiency associated with ornithine transcarbamylase deficiency
    • Mayatepek E, Kurczynski TW, Hoppel CL, Gunning WT. Carnitine deficiency associated with ornithine transcarbamylase deficiency. Pediatr Neurol 7:196-199, 1991.
    • (1991) Pediatr Neurol , vol.7 , pp. 196-199
    • Mayatepek, E.1    Kurczynski, T.W.2    Hoppel, C.L.3    Gunning, W.T.4
  • 16
    • 0025339637 scopus 로고
    • Hypocarnitinémie chez les patients atteints d'un défaut primaire du métabolisme de l'ammoniaque traités avec le benzoate de sodium
    • Michalak A, Lambert MA, Dallaire L et al. Hypocarnitinémie chez les patients atteints d'un défaut primaire du métabolisme de l'ammoniaque traités avec le benzoate de sodium. Diabete Metab 16:226-233, 1990.
    • (1990) Diabete Metab , vol.16 , pp. 226-233
    • Michalak, A.1    Lambert, M.A.2    Dallaire, L.3
  • 17
    • 0023836662 scopus 로고
    • Secondary carnitine deficiency in hyperammonemic attacks of ornithine transcarbamylase deficiency
    • Ohtani Y, Ohyanagi K, Yamamoto S, Matsuda I. Secondary carnitine deficiency in hyperammonemic attacks of ornithine transcarbamylase deficiency. J Pediatr 112:409-414, 1988.
    • (1988) J Pediatr , vol.112 , pp. 409-414
    • Ohtani, Y.1    Ohyanagi, K.2    Yamamoto, S.3    Matsuda, I.4
  • 18
    • 0026498551 scopus 로고
    • Hyperammonemia-hyperornithinemia-homocitrullinuria syndrome: Neurologie, ophtalmologic and neuropsychologic examination of six patients
    • Lemay JF, Lambert MA, Mitchell GA et al. Hyperammonemia-hyperornithinemia-homocitrullinuria syndrome: Neurologie, ophtalmologic and neuropsychologic examination of six patients. J Pediatr 121:725-730, 1992.
    • (1992) J Pediatr , vol.121 , pp. 725-730
    • Lemay, J.F.1    Lambert, M.A.2    Mitchell, G.A.3
  • 19
    • 0000147466 scopus 로고
    • An ion exchange method for plasma ammonia concentration
    • Dienst SG. An ion exchange method for plasma ammonia concentration. J Lab Clin Med 58:149-155, 1961.
    • (1961) J Lab Clin Med , vol.58 , pp. 149-155
    • Dienst, S.G.1
  • 20
    • 13344254839 scopus 로고
    • Determination of the concentration of ammonia nitrogen in plasma by means of a simple ion exchange method
    • Miller GE, Rice JD Jr. Determination of the concentration of ammonia nitrogen in plasma by means of a simple ion exchange method. Tech Bull Regist Med Tech 32:203-209, 1962.
    • (1962) Tech Bull Regist Med Tech , vol.32 , pp. 203-209
    • Miller, G.E.1    Rice Jr., J.D.2
  • 21
    • 0017071784 scopus 로고
    • An improved and simplified radioisotopic assay for the determination of free and esterified carnitine
    • McGarry JD, Foster DW. An improved and simplified radioisotopic assay for the determination of free and esterified carnitine. J Lipid Res 17:277-281, 1976.
    • (1976) J Lipid Res , vol.17 , pp. 277-281
    • McGarry, J.D.1    Foster, D.W.2
  • 22
    • 0024344870 scopus 로고
    • Application of fast atom bombardment with tandem mass spectrometry and liquid chromatography/mass spectrometry to the analysis of acylcarnitines in human urine, blood and tissue
    • Millington DS, Norwood DL, Kodo N, Roe CR, Inowe F. Application of fast atom bombardment with tandem mass spectrometry and liquid chromatography/mass spectrometry to the analysis of acylcarnitines in human urine, blood and tissue. Anal Biochem 180:331-339, 1989.
    • (1989) Anal Biochem , vol.180 , pp. 331-339
    • Millington, D.S.1    Norwood, D.L.2    Kodo, N.3    Roe, C.R.4    Inowe, F.5
  • 23
    • 0015317629 scopus 로고
    • Direct colorimetric determination of hippuric acid in urine
    • Tomokuni K, Ogata M. Direct colorimetric determination of hippuric acid in urine. Clin Chem 18:349-351, 1972.
    • (1972) Clin Chem , vol.18 , pp. 349-351
    • Tomokuni, K.1    Ogata, M.2
  • 24
    • 0026550814 scopus 로고
    • Availability of glycine and coenzyme A limits glycine conjugation in vivo
    • Gregus Z, Fekete T, Varga F, Klaassen CD. Availability of glycine and coenzyme A limits glycine conjugation in vivo. Drug Metab Dispos 20:234-240, 1992.
    • (1992) Drug Metab Dispos , vol.20 , pp. 234-240
    • Gregus, Z.1    Fekete, T.2    Varga, F.3    Klaassen, C.D.4
  • 25
    • 0023622455 scopus 로고
    • Urinary excretion of 5-oxoproline (pyroglutamic aciduria) as an index of glycine insufficiency in normal man
    • Jackson AA, Badaloo AV, Forrester T, Hibbert JM, Persaud C. Urinary excretion of 5-oxoproline (pyroglutamic aciduria) as an index of glycine insufficiency in normal man. Br J Nutr 58:207-214, 1987.
    • (1987) Br J Nutr , vol.58 , pp. 207-214
    • Jackson, A.A.1    Badaloo, A.V.2    Forrester, T.3    Hibbert, J.M.4    Persaud, C.5
  • 26
    • 0022341337 scopus 로고
    • Benzoylalanine: Detection and identification of an alanine conjugate with benzoic acid in hyperammonemic patients treated with sodium benzoate
    • Shinka T, Inoue Y, Kuhara T, Matsumoto M, Matsumoto I. Benzoylalanine: detection and identification of an alanine conjugate with benzoic acid in hyperammonemic patients treated with sodium benzoate. Clin Chim Acta 151:293-300, 1985.
    • (1985) Clin Chim Acta , vol.151 , pp. 293-300
    • Shinka, T.1    Inoue, Y.2    Kuhara, T.3    Matsumoto, M.4    Matsumoto, I.5
  • 28
    • 13344273228 scopus 로고
    • Benzoic aciduria in chronic psychoses
    • Edinburgh: Churchill Livingstone, (Stern J, Toothill C, Eds.)
    • Perry T, Hansen S, Lesk D. Benzoic aciduria in chronic psychoses. In Edinburgh: Churchill Livingstone, "Organic acidurias" (Stern J, Toothill C, Eds.), 1972, pp 99-112.
    • (1972) Organic Acidurias , pp. 99-112
    • Perry, T.1    Hansen, S.2    Lesk, D.3
  • 29
    • 0027765518 scopus 로고
    • Conjugation of benzoic acid with glycine in human liver and kidney: A study on the interindividual variability
    • Temellini A, Mogavero S, Giulianotti PC, Pietrabissa A, Mosca F, Pacifici GM. Conjugation of benzoic acid with glycine in human liver and kidney: A study on the interindividual variability. Xenobiotica 23:1427-1433, 1993.
    • (1993) Xenobiotica , vol.23 , pp. 1427-1433
    • Temellini, A.1    Mogavero, S.2    Giulianotti, P.C.3    Pietrabissa, A.4    Mosca, F.5    Pacifici, G.M.6
  • 30
  • 31
    • 0025880345 scopus 로고
    • Alteration of urinary carnitine profile induced by benzoate administration
    • Sakuma T. Alteration of urinary carnitine profile induced by benzoate administration. Arch Dis Child 66:873-875, 1991.
    • (1991) Arch Dis Child , vol.66 , pp. 873-875
    • Sakuma, T.1


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.