A mouse model of gyrate atrophy of the choroid and retina: Early retinal pigment epithelium damage and progressive retinal degeneration

Journal of Clinical Investigation

Volumn 97, Issue 12, 1996, Pages 2753-2762

  Wang, Tao ^a   Milam, Ann H ^b   Steel, Gary ^a   Valle, David ^a,c  

^a JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF WASHINGTON SCHOOL OF MEDICINE   (United States)

^c JOHNS HOPKINS UNIVERSITY   (United States)

Author keywords

histopathology; inborn error; ornithine; ornithine aminotransferase; pathophysiology

Indexed keywords

ORNITHINE OXOACID AMINOTRANSFERASE;

ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CHOROID GYRATE ATROPHY; CONTROLLED STUDY; ELECTRON MICROSCOPY; ELECTRORETINOGRAPHY; ENZYME DEFICIENCY; FEMALE; GENE TARGETING; HYPERORNITHINEMIA; MOUSE; NONHUMAN; PHAGOSOME; PIGMENT CELL; PRIORITY JOURNAL; RETINA DEGENERATION; RETINA GYRATE ATROPHY; RETINA ROD OUTER SEGMENT;

EID: 0029970085     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI118730     Document Type: Article

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