Inhibition of phosphomannose isomerase by fructose 1-phosphate: An explanation for defective N-glycosylation in hereditary fructose intolerance

Pediatric Research

Volumn 40, Issue 5, 1996, Pages 764-766

  Jaeken, Jaak ^a,d   Pirard, Michel ^b   Adamowicz, Maciej ^c   Pronicka, Ewa ^c   Van Schaftingen, Emile ^b  

^a UNIVERSITY OF LEUVEN   (Belgium)

^b UNIVERSITÉ CATHOLIQUE DE LOUVAIN   (Belgium)

^c CHILDREN'S MEMORIAL HEALTH INSTITUTE   (Poland)

^d UNIVERSITY HOSPITALS LEUVEN   (Belgium)

Author keywords

[No Author keywords available]

Indexed keywords

ENZYME INHIBITOR; FRUCTOSE 1 PHOSPHATE; MANNOSE PHOSPHATE ISOMERASE; TRANSFERRIN;

ARTICLE; CONGENITAL DISORDER OF GLYCOSYLATION; ENZYME DEFICIENCY; ENZYME INHIBITION; GALACTOSEMIA; GLYCOSYLATION; HEREDITARY FRUCTOSE INTOLERANCE; HUMAN; ISOELECTRIC FOCUSING; PRIORITY JOURNAL;

EID: 0029957579     PISSN: 00313998     EISSN: None     Source Type: Journal    
DOI: 10.1203/00006450-199611000-00017     Document Type: Article

References (14)

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