Glanzmann thrombasthenia due to a two amino acid deletion in the fourth calcium-binding domain of α(IIb): Demonstration of the importance of calcium-binding domains in the conformation of α(IIb)β3

Blood

Volumn 88, Issue 1, 1996, Pages 167-173

  Basani, Ramesh B ^b   Vilaire, Gaston ^b   Shattil, Sanford J ^b   Kolodziej, Michael A ^b   Bennett, Joel S ^b   Poncz, Mortimer ^a  

^a CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

^b NONE

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID; CALCIUM BINDING PROTEIN; GLYCOPROTEIN IIB; INTEGRIN; MUTANT PROTEIN; PROTEIN SUBUNIT;

ALLELE; ANIMAL CELL; ARTICLE; CASE REPORT; CELL SURFACE; CONTROLLED STUDY; DELETION MUTANT; GLANZMANN DISEASE; HUMAN; INTRACELLULAR TRANSPORT; MONKEY; NEWBORN; NONHUMAN; PRIORITY JOURNAL; PROTEIN CONFORMATION; PROTEIN DOMAIN; THROMBOCYTE AGGREGATION;

EID: 0029947855     PISSN: 00064971     EISSN: None     Source Type: Journal    
DOI: 10.1182/blood.v88.1.167.bloodjournal881167     Document Type: Article

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