Biochemical investigations and immunoblot analyses of two unrelated patients with an isolated deficiency in complex II of the mitochondrial respiratory chain

Biochemical and Biophysical Research Communications

Volumn 220, Issue 1, 1996, Pages 57-62

  Birch Machin, M A ^a,d   Marsac, C ^a   Ponsot, G ^b   Parfait, B ^a   Taylor, R W ^c   Rustin, P ^a   Munnich, A ^a  

^a HÔPITAL NECKER ENFANTS MALADES   (France)

^b HÔPITAL SAINT VINCENT DE PAUL   (France)

^c NEWCASTLE UNIVERSITY   (United Kingdom)

^d ROYAL VICTORIA INFIRMARY   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ENZYME ANTIBODY; SUCCINATE DEHYDROGENASE (UBIQUINONE);

ARTICLE; CASE REPORT; CHILD; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME DEFICIENCY; ENZYME SUBUNIT; FEMALE; HUMAN; HUMAN TISSUE; IMMUNOBLOTTING; MITOCHONDRIAL RESPIRATION; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN CONTENT; RESPIRATORY CHAIN;

EID: 0029931901     PISSN: 0006291X     EISSN: None     Source Type: Journal    
DOI: 10.1006/bbrc.1996.0356     Document Type: Article

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