Left and right ventricular dysplasia and Uhl's anomaly: A case report

American Journal of Forensic Medicine and Pathology

Volumn 17, Issue 2, 1996, Pages 141-145

  Sutter, A ^a   Gujer, H R ^a  

^a UNIVERSITY OF LAUSANNE   (Switzerland)

Author keywords

Left ventricular dysplasia; Right ventricular dysplasia; Sudden death; Uhl's anomaly

Indexed keywords

ADULT; ARTICLE; AUTOPSY; CASE REPORT; CAUSE OF DEATH; CONGENITAL HEART MALFORMATION; DYSPLASIA; HEMOSTASIS; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; LUNG EDEMA; MALE; SUDDEN DEATH; UHL ANOMALY;

ADULT; AGE FACTORS; DEATH, SUDDEN, CARDIAC; FATAL OUTCOME; HEART DEFECTS, CONGENITAL; HEART VENTRICLES; HUMANS; MALE; SEX FACTORS; VENTRICULAR DYSFUNCTION, LEFT; VENTRICULAR DYSFUNCTION, RIGHT;

EID: 0029926728     PISSN: 01957910     EISSN: None     Source Type: Journal    
DOI: 10.1097/00000433-199606000-00011     Document Type: Article

References (27)

1. Osler WM. The principles and practice of medicine. 6th ed, New York: Appleton-Century-Crofts, 1905:820.
2. Segall HN. Parchment heart (Osler). Am Heart J 1950;40: 948-50.
3. Waller BF, Smith ER, Blackbourne BD, Arce FP, Sarkar NN, Roberts WC. Congenital hypoplasia of portions of both right and left ventricular myocardial walls. Am J Car- diol 1980;46:885-91.
4. Bharati S, Ciraulo DA, Bilitch M, Rosen KM, Leu M. Inexcitable right ventricule and bilateral boundle brande block in disease. Circulation 1978;57:636-44.
5. Grüter J, Jornod J, Enrico JF, Baumann RP. Dysplasie K ventriculaire arythmogéne ou maladie de Uhl? Schweiz Med Wochenschr 1989;119:582-7.
6. Uhl HSM. Previously undescribed congenital malforma- tion of the heart: almost total absence of the myocardium of the right ventricle. Bull Johns Hopkins Hasp 1952;91: 197-205.
7. Castelman B, Sprague HB. Case records of the Massachu- setts General Hospital. Weekly clinicopathological exer- cises. N Engl J Med 1952;246:785-90.
8. Goul DK, Guttman AB, Carrasco J, Lyon AF. Partial ab- sence of the right ventricular musculature: a congenital lesion. Am J Med 1967;42:636-41.
9. Reeve R, MacDonald D. Partial absence of the right ven- tricular musculature: partial parchment heart. Am J Car- diol 1964;14:415-9.
10. Segiura M, Hayashi T, Ueno K. Partial absence of the right ventricular muscle in an aged. Jpn Heart J 1970;11:582-5.
11. Virmani R, Robinowitz M, Clark MA, MacAllister HA. Sudden death and partial absence of the right ventricular myocardium. Arch Pathol Lab Med 1982;106:163-7.
12. Neimann N, Pernot C, Rauber G. Aplasie du myocarde du ventricule droit. Arch Mal Coeur 1965;58:421-30.
13. Vecht RJ, Carmichael JS, Gopal R, Philip G. Uhl's anomaly. Br Heart J 1979;41:676-82.
14. Obma R, Perry LW, Scott LR. Uhl's anomaly of the heart with atrial septal defect and valvular pulmonary stenosis. Med Ann DC 1974;43:413-8.
15. Haworth SG, Shinebourne EA, Miller GAH. Right to left interatrial shunting with normal right ventricular pressure. Br Heart J 1975;37:386-91.
16. Diaz LP, Jimenez MQ, Granados FM, Martinez VP, Batres GM. Congenital absence of myocardium of right ventricle: Uhl's anomaly. Br Heart J 1973;35:570-2.
17. Novak G, Szanto PB, Gasul B, Dillion E. Congenital aplasia of the myocardium of the right ventricular. Proc Inst Med Chir 1957;21:334-9.
18. Arcilia RA, Gashl BM. Congenital aplasia or marked hypoplasia of the myocardium. J Pediatr 1961;58:381-8.
19. Vedel J, Frank R, Fontaine G, et al. Tachycardies ventriculaires recidivantes et ventricule droit papyracé de l'adulte. Arch Mal Coeur 1978;71:973-81.
20. Hoback J, Adicoff A, From AHL, Mc Kamy Smith, Shafer R, Chesler E. A report of Uhl's disease in identical adult twins. Chest 1981;79:306-10.
21. Davis CL. Development of the human heart from its first appearance to the stage found in embryos of twenty paired somites. Carnegie Inst Wash 1927;19:245.
22. Ostermeyer F. Uhl's disease: partial parchment right ventricle. Virchows Arch [A] 1974;362:185-94.
23. Froment R, Perrin A, Loire R, Dalloz CL. Ventricule droit papyracé du jeune adulte par dystrophie congénitale. Arch Mal Coeur 1968;61:477-503.
24. Waynberger M, Courtadon M, Pellier JM, Ducloux G, Jallut H, Slama R. Tachycardie ventriculaire familiale. A propos de 7 cas. Nouv Presse Med 1974;3:1857-60.
25. Diggelmann U, Baur HR. Familial Uhl's anomaly in the adult. Am J Cardiol 1984;53:1402-3.
26. Fontaine G, Guirandon G, Frank R, et al. Dysplasie ventriculaire droite arythmogène et maladie de Uhl. Arch Mal Coeur 1982;4:361-72.
27. Marcus FI, Fontaine G, Guirandon G, et al. Right ventricular dysplasia. A report of 24 cases. Circulation 1982;69:384.