Detection of gp91-phox precursor protein in B-cell lines from patients with X-linked Chronic Granulomatous Disease as an indicator for mutations impairing cytochrome b558 biosynthesis

Biochemical Journal

Volumn 315, Issue 2, 1996, Pages 571-575

  Porter, Colin D ^a,c   Kuribayashi, Futoshi ^b,d   Parkar, Mohamed H ^a,e   Roos, Dirk ^b   Kinnon, Christine ^a  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

^b UNIVERSITY OF AMSTERDAM   (Netherlands)

^c INSTITUTE OF CANCER RESEARCH   (United Kingdom)

^d KYUSHU UNIVERSITY   (Japan)

^e UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

CYTOCHROME B; GLYCOPROTEIN; PROTEIN PRECURSOR; PROTEIN SUBUNIT; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE PHOSPHATE OXIDASE;

ARTICLE; B LYMPHOCYTE; BIOSYNTHESIS; CHRONIC GRANULOMATOUS DISEASE; GENE; HUMAN; HUMAN CELL; POINT MUTATION; PRIORITY JOURNAL; PROTEIN DOMAIN; PROTEIN SYNTHESIS;

AMINO ACID SEQUENCE; B-LYMPHOCYTES; BINDING SITES; CELL LINE; CYTOCHROME B GROUP; GRANULOMATOUS DISEASE, CHRONIC; HEME; HUMANS; LINKAGE (GENETICS); MEMBRANE GLYCOPROTEINS; MEMBRANE TRANSPORT PROTEINS; MOLECULAR SEQUENCE DATA; MOLECULAR STRUCTURE; MUTATION; NADPH DEHYDROGENASE; NADPH OXIDASE; PHOSPHOPROTEINS; PROTEIN CONFORMATION; PROTEIN PRECURSORS; SEQUENCE HOMOLOGY, AMINO ACID; X CHROMOSOME;

EID: 0029923194     PISSN: 02646021     EISSN: None     Source Type: Journal    
DOI: 10.1042/bj3150571     Document Type: Article

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