Anaesthetic management in maple syrup urine disease

Anaesthesia

Volumn 51, Issue 6, 1996, Pages 575-578

  Kahraman, S ^a   Ercan, M ^a   Akkus O ^a   Ercelen O ^a   Erdem, K ^a   Coskun T ^a  

^a HACETTEPE UNIVERSITY   (Turkey)

Author keywords

Complications; maple syrup urine disease; Intravenous anaesthetics; ketamine, propofol

Indexed keywords

ANESTHETIC AGENT; KETAMINE; PROPOFOL;

ANESTHESIA; ARTICLE; CASE REPORT; CONVULSION; ELECTIVE SURGERY; EMERGENCY SURGERY; FEMALE; HUMAN; MALE; MAPLE SYRUP URINE DISEASE; PATHOPHYSIOLOGY; PEDIATRIC SURGERY; PRESCHOOL CHILD;

ANESTHESIA, GENERAL; ANESTHESIA, INTRAVENOUS; ANESTHETICS, DISSOCIATIVE; ANESTHETICS, INTRAVENOUS; CARBON DIOXIDE; CHILD, PRESCHOOL; FEMALE; HUMANS; INFANT; KETAMINE; MALE; MAPLE SYRUP URINE DISEASE; OXYGEN; PARTIAL PRESSURE; PROPOFOL; RISK FACTORS;

EID: 0029920238     PISSN: 00032409     EISSN: None     Source Type: Journal    
DOI: 10.1111/j.1365-2044.1996.tb12568.x     Document Type: Article

References (26)

1. CHUANG DT, SHIH VE. Disorders of branched chain amino acid and keto acid metabolism. In: SCRIVER CR, BEAUDET AL, SLY WS, VALLE D, eds. The metabolic and molecular basis of inherited disease. New York: McGraw-Hill Inc., 1995: 1239-77.
2. ÖZALP I, COSKUN T. TOKOL S. DEMIRCIN G, MÖNCH E. Inherited metabolic disorders in Turkey. Journal of lnherited Metabolic Diseases 1990; 13: 732-8.
3. THOMPSON JN, FRANCIS DEM, HALLIDAY D. Acute illness in maple syrup urine disease. Dynamics of protein metabolism and implications for management. Journal of Pediatrics 1991: 119: 35-41.
4. BERRY GT, HEIDENREICH R, KAPLAN P, LEVINE F, MAZUR A, PALMIERI MJ, YUDKOFF M, SEGAL S. Branched-chain amino acid-free parenteral nutrition in the treatment of acute metabolic decompensation in patients with maple syrup urine disease. New England Journal of Medicine 1991; 321: 175-9.
5. KAPLAN P, MAZUR A, FIELD M, BERLIN JA, BERRY GT, HEIDENREICH R, YUDKOFF M, SEGAL S. Intellectual outcome in children with maple syrup urine disease. Journal of Pediatrics 1991; 119: 46-50.
6. LANGENBECK U. Pathobiochemical and pathophysiological analysis of the MSUD phenotype. In: ABIDI SA, FEKL W, LANGENBECK U, SCHAUDER P, eds. Branched-chain amino and keto acids in health and disease. Basel: Karger, 1984: 315-34.
7. WENDEL U. Disorders of branched-chain amino acid metabolism. In: FERRANDES J, SAUDUBRAY JM, TADA K, eds. Inborn metabolic diseases. Diagnosis and treatment. Berlin. Heidelberg: Springer-Verlag, 1990: 265-70.
8. LEVIN ML, SCHEIMANN A, LEWIS RA, BEAUDET AL. Cerebral edema in maple syrup urine disease. Journal of Pediatrics 1993; 122: 167.
9. MANTOVANI JF, NAIDICH TP, PRENSKY AL, DODSON WE, WILLIAMS JC. MSUD: presentation with pseudotumor cerebri and CT abnormalities. Journal of Pediatrics 1980; 96: 279-81.
10. LUNGAROTTI MS, SIGNORINI E, GARIBANDI LR. Cerebral edema in maple syrup urine disease. American Journal of Diseases of Children 1982; 136: 648.
11. MIKATI MA, DUDIN GE, DER KALOUSTIAN VM. Maple syrup urine disease with increased intracranial pressure. American Journal of Diseases of Children 1982; 136: 6423.
12. RIVIELLO JJ JR, REZVANI I, DIGEORGE AM, FOLEY CM. Cerebral edema causing death in children with maple syrup urine disease. Journal of Pediatrics 1991; 119: 42-5.
13. WENDEL U, LANGENBECK U, LOMBECK I, BREMER HJ. Maple syrup urine disease: therapeutic use of insulin in catabolic states. European Journal of Pediatrics 1982; 139: 172-5.
14. SNYDERMAN SE. Treatment outcome of maple syrup urine disease. Acta Paediatrica Japonica 1988; 30: 417-24.
15. CLOW CL, READE TM, SERIVER CR. Outcome of early and long-term management of classical maple syrup urine disease. Paediatrics 1981; 68: 856-62.
16. GOODMAN SI. Inherited metabolic disease in the newborn. Approach to diagnosis and management. Advances in Pediatrics 1986; 33: 197-224.
17. THOMPSON GN, BUTT WW, SHANN FA, KIRBY DM, HENNING RD, HOWELLS DW, OSBORNE A. Continuous venovenous hemofiltration in the management of acute decomposition in inborn errors of metabolism. Journal of Pediatrics 1991; 118: 879-84.
18. RUTLEDGE SL, HAVENS PL, HAYMOND MW, MCLEAN RH, KAN JS, BRUSILOW SW. Neonatal haemodialysis: effective therapy for the encephalopathy of inborn errors of metabolism. Journal of Pediatrics 1990; 116: 125-8.
19. SYBERT JW, KYFF JV. Ketamine treatment of status epilepticus. Anesthesiology 1983; 58: 203.
20. FISCHER M MCD. Use of ketamine hydrochloride in the treatment of convulsions. Anaesthesia and Intensive Cure 1974; 2: 266 -8.
21. REDER BS, TRAPP LS, TRALITMAN KC. Ketamine suppression of chemical induced convulsions in the two-day-old white leghorn cockerel. Anesthesia and Analgesia 1980; 59: 406-9.
22. KAYAMA Y, IWAMA K. The EEG evoked potentials and single unit activity during ketamine anesthesia in cats. Anesthesiology 1972; 36: 316-28.
23. FERRER-ALLADO T, BRECHNER VL, DYMOND A, COZHN H, CRANDALL P. Ketamine-induced electroconvulsive phenomena in the human limbic and thalamic region. Anesthesiology 1973; 38: 333-4.
24. CORRSEN G. LITTLE S, TAVAKOLI M. Ketamine and epilepsy. Anesthesia and Analgesia 1974; 53: 319-35.
25. MORTON H. MSUD news from the clinic for special children. Maple Syrup Urine Disease Newsletter 1992; 10: 9-11.
26. FUKUTOMI M, KITAMURA S, KAWACHI K, TSUJI T, HASHIMOTO K, YOSHIOKA A. Successful repair and postoperative management of tetralogy of Fallot in a patient with maple syrup urine disease. Heart-Vessels (1993; 8: 48-51.