Proton magnetic resonance spectroscopy on childhood-onset dentatorubral-pallidoluysian atrophy (DRPLA)

Brain and Development

Volumn 18, Issue 2, 1996, Pages 142-146

  Miyazaki, Masahito ^a   Hashimoto, Toshiaki ^a,b   Yoneda, Yoshihiro ^a   Tayama, Masanobu ^a   Harada, Masafumi ^a   Miyoshi, Hirokazu ^a   Kawano, Noboru ^c   Murayama, Nobuhiro ^d   Kondo, Ikuko ^d   Kuroda, Yasuhiro ^a  

^a UNIVERSITY OF TOKUSHIMA   (Japan)

^b National Center of Neurology and Psychiatry   (Japan)

^c National Hospital Organization   (Japan)

^d EHIME UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

1H MRS; Childhood onset; DRPLA; NAA Cr; Progressive myoclonus epilepsy

Indexed keywords

CHOLINE; CREATINE; N ACETYLASPARTIC ACID;

ADOLESCENT; ADULT; ARTICLE; BASAL GANGLION; BRAIN DYSFUNCTION; CASE REPORT; CELL LOSS; DENTATORUBROPALLIDOLUYSIAN ATROPHY; DIAGNOSTIC VALUE; DISEASE SEVERITY; DNA DETERMINATION; FEMALE; HEREDITY; HUMAN; MALE; MYOCLONUS EPILEPSY; NERVE CELL; ONSET AGE; PARIETAL LOBE; PATHOPHYSIOLOGY; PROTON NUCLEAR MAGNETIC RESONANCE;

EID: 0029917561     PISSN: 03877604     EISSN: None     Source Type: Journal    
DOI: 10.1016/0387-7604(95)00115-8     Document Type: Article

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