The relationship between the fibrinogen D domain self-association/cross-linking site (γXL) and the fibrinogen Dusart abnormality (Aα R554C-albumin): Clues to thrombophilia in the "Dusart syndrome"

Journal of Clinical Investigation

Volumn 97, Issue 10, 1996, Pages 2342-2350

  Mosesson, Michael W ^a,f   Siebenlist, Kevin R ^a   Hainfeld, James F ^b   Wall, Joseph S ^b   Soria, Jeanette ^c   Soria, Claudine ^d   Caen, Jacques P ^e  

^a UNIVERSITY OF WISCONSIN SCHOOL OF MEDICINE AND PUBLIC HEALTH   (United States)

^b BROOKHAVEN NATIONAL LABORATORY   (United States)

^c HÔTEL DIEU   (France)

^d HÔPITAL LARIBOISIÈRE   (France)

^e Institut des Vaisseaux et du Sang   (France)

^f AURORA SINAI MEDICAL CENTER   (United States)

Author keywords

Factor XIII; Fibrin; Fibrinogen; Plasminogen; Thrombophilia

Indexed keywords

BLOOD CLOTTING FACTOR 13; DEXTRAN; FIBRIN; FIBRINOGEN VARIANT; GLYCEROL; PLASMINOGEN;

ARTICLE; CARBOXY TERMINAL SEQUENCE; CONTROLLED STUDY; FIBRIN POLYMERIZATION; FIBRINOGEN DEFECT; HUMAN; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN CROSS LINKING; PROTEIN DOMAIN; THROMBOPHILIA;

DEXTRANS; FIBRIN FIBRINOGEN DEGRADATION PRODUCTS; FIBRINOGENS, ABNORMAL; GLYCEROL; HUMANS; MICROSCOPY, ELECTRON, SCANNING TRANSMISSION; PLASMINOGEN; THROMBOSIS;

EID: 0029885335     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI118677     Document Type: Article

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