Lymphangioleiomyomatosis: The pathophysiology of diminished exercise capacity

American Journal of Respiratory and Critical Care Medicine

Volumn 153, Issue 4, 1996, Pages 1368-1376

  Crausman, Robert S ^b   Jennings, Constance A ^b   Mortenson, Rebecca L ^b   Ackerson, Lynn M ^b   Irvin, Charles G ^b   King Jr , Talmadge E ^a  

^a NATIONAL JEWISH MEDICAL AND RESEARCH CENTER   (United States)

^b NONE

Author keywords

[No Author keywords available]

Indexed keywords

OXYGEN;

ADULT; ARTERIAL GAS; ARTICLE; BLOOD PRESSURE; CLINICAL ARTICLE; CONTROLLED STUDY; EXERCISE TOLERANCE; FEMALE; HEART RATE; HUMAN; LEIOMYOMATOSIS; LUNG DEAD SPACE; LUNG DIFFUSION CAPACITY; LUNG DISEASE; LUNG FUNCTION TEST; LUNG GAS EXCHANGE; LUNG MINUTE VOLUME; LYMPHANGIOMYOMA; OXYGEN CONSUMPTION; PATHOPHYSIOLOGY; PRIORITY JOURNAL; RESIDUAL VOLUME; TIDAL VOLUME; TOTAL LUNG CAPACITY;

EID: 0029878721     PISSN: 1073449X     EISSN: None     Source Type: Journal    
DOI: 10.1164/ajrccm.153.4.8616568     Document Type: Article

References (22)

1. Viskum, K. 1993. Pulmonary lymphangioleiomyomatosis. Monaldi Arch. Chest Dis. 48:233-236.
2. Stovin, P., C. Lum, D. Flower, C. Darke, and M. Beeley. 1975. The lungs in lymphangiomyomatosis and tuberous sclerosis. Thorax 30:497-509.
3. Templeton, P. A., T. C. McLoud, N. L. Muller, J. A. Shepard, and E. H. Moore. 1989. Pulmonary lymphangioleiomyomatosis: CT and pathologic findings. J. Comput. Assist. Tomogr. 13:54-57.
4. Chan, J. K. C., W. Y. W. Tsang, M. Y. Pau, M. C. Tang, S. W. Pang, and C. D. M. Fletcher. 1993. Lymphangiomyomatosis and angiomyolipoma: closely related entities characterized by hamartomatous proliferation of HMB-45-positive smooth muscle. Histopathology 22:445-455.
5. Sobonya, R., Q. Stuart, and J. Fleishman. 1985. Pulmonary lymphangioleiomyomatosis: quantitative analysis of lesions producing air flow limitation. Hum. Pathol. 16:1122-1128.
6. Poh, S. C., and S. C. Chiang. 1979. Pulmonary lymphangioleiomyomatosis. Singapore Med. J. 20:460-464.
7. Taylor, J. R., J. Ryu, T. V. Colby, and T. A. Raffin. 1990. Lymphangioleiomyomatosis. Clinical course in 32 patients. N. Engl. J. Med. 323:1254-1260.
8. Corrin, B., A. Liebow, and P. Friedman. 1975. Pulmonary lymphangioleiomyomatosis: a review. Am. J. Pathol. 79:348-382.
9. Bush, J., R. McLean, and H. Sieker. 1969. Diffuse lung disease due to lymphangiomyoma Am. J. Med. 46:645-654.
10. Carrington, C. B., D. W. Cugell, E. A. Gaensler, A. Marks, R. A. Redding, J. T. Schaaf, and A. Tomasian. 1977. Lymphangioleiomyomatosis. Physiologic-pathologic-radiologic correlations. Am. Rev. Respir. Dis. 116:977-995.
11. Fukuda, Y., M. Kawamoto, A. Yamamoto, M. Ishizaki, F. Basset, and Y. Masugi. 1990. Role of elastic fiber degradation in emphysemalike lesions of pulmonary lymphangiomyomatosis. Hum. Pathol. 21: 1252-1261.
12. Schiavina, M., S. Pileri, and A. M. Mancini. 1986. Lymphangioleiomyomatosis. A case report with an immunohistochemical study. Appl. Pathol. 4:170-174.
13. Schiavina, M., A. Fabiani, B. Cornia, E. DeBenedictis, V. Poletti, S. Pileri, and M. Zompatori. 1994. Lymphangioleiomyomatosis: clinical course. Monaldi Arch. Chest Dis. 49:6-14.
14. Raymond, A. A., M. R. Isa, T. Abdullah, and M. V. Kudva. 1993. Lymphangioleiomyomatosis with chylous ascites. Singapore Med. J. 34:276-278.
15. Merino Mujica, J. M., and M. Olivera Fernandez. 1992. Chyluria and lymphangioleiomyomatosis (letter). Rev. Clin. Esp. 190:382.
16. Lack, E. E., M. F. Dolan, J. Finisio, G. Grover, M. Singh, and T. J. Triche. 1986. Pulmonary and extrapulmonary lymphangioleiomyomatosis. Report of a case with bilateral renal angiomyolipomas, multifocal lymphangioleiomyomatosis, and a glial polyp of the endocervix. Am. J. Surg. Pathol. 10:650-657.
17. Kerr, L. A., M. L. Blute, J. H. Ryu, S. J. Swensen, and R. S. Malek. 1993. Renal angiomyolipoma in association with pulmonary lymphangioleiomyomatosis: forme fruste of tuberous sclerosis? Urology 41: 440-444.
18. Jozwiak, S. 1990. Pulmonary lymphangioleiomyomatosis: a "forme fruste" of tuberous sclerosis? (letter). Am. J. Roentgenol. 155:419.
19. Cagnano, M., D. Benharroch, and D. B. Geffen, 1991. Pulmonary lymphangioleiomyomatosis. Report of a case with associated multiple soft-tissue tumors. Arch. Pathol. Lab. Med. 115:1257-1259.
20. Brieler, H. S., E. W. Schwarze, C. Stambolis, H. Haage, and A. Thiede. 1975. Lymphangioleiomyomatosis. Langenbecks Arch. Chir. 339: 642-643.
21. Berger, J. L., and M. I. Shaff. 1981. Pulmonary lymphangioleiomyomatosis. J. Comput. Assist. Tomogr. 5:565-567.
22. Crausman, R. S., D. A. Lynch, R. L. Mortenson, C. G. Irvin, C. A. Jennings, D. C. Ellegood, V. A. E. Hale, T. E. King, Jr., and J. D. Newell. 1994. Quantitative CT analysis predicts the degree of pulmonary dysfunction in lymphangioleiomyomatosis (LAM) (abstract). Am. Rev. Respir. Dis. 149:A877.