Dermal fibroblast culture as a model system for studies of fibrillin assembly and pathogenetic mechanisms: Defects in distinct groups of individuals with Marfan's syndrome

Laboratory Investigation

Volumn 75, Issue 3, 1996, Pages 389-402

  Brenn, Thomas ^a,d   Aoyama, Takeshi ^a,e   Francke, Uta ^a   Furthmayr, Heinz ^b,c  

^a Department of Pathology   (United States)

^b STANFORD UNIVERSITY MEDICAL CENTER   (United States)

^c STANFORD UNIVERSITY   (United States)

^d RWTH AACHEN UNIVERSITY   (Germany)

^e KYOTO UNIVERSITY   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

FIBRILLIN;

ARTICLE; CELL DENSITY; CONTROLLED STUDY; EXTRACELLULAR MATRIX; FIBROBLAST CULTURE; GENE MUTATION; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOELECTRON MICROSCOPY; IMMUNOFLUORESCENCE; MARFAN SYNDROME; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN ASSEMBLY; SKIN BIOPSY; SKIN FIBROBLAST;

ANTIBODIES; ANTIBODY SPECIFICITY; CELLS, CULTURED; EXTRACELLULAR MATRIX; EXTRACELLULAR MATRIX PROTEINS; FIBROBLASTS; FLUORESCENT ANTIBODY TECHNIQUE, INDIRECT; HUMANS; MARFAN SYNDROME; MICROFILAMENT PROTEINS; MICROSCOPY, IMMUNOELECTRON; PRECIPITIN TESTS; SKIN; SOLUBILITY; TRYPSIN;

EID: 0029833257     PISSN: 00236837     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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