Dystrophin-associated protein abnormalities in dystrophin-deficient muscle fibers from symptomatic and asymptomatic Duchenne/Becker muscular dystrophy carriers

Acta Neuropathologica

Volumn 92, Issue 4, 1996, Pages 369-377

  Di Blasi, C ^a   Morandi, L ^a   Barresi, R ^a   Blasevich, F ^a   Cornelio, F ^a   Mora, M ^a  

^a Ist Naz Neurologico C Besta ^*  (Italy)

Author keywords

Becker muscular dystrophy; Duchenne muscular dystrophy; Dystroglycan; Dystrophin associated proteins; Sarcoglycans

Indexed keywords

ALPHA SARCOGLYCAN; BETA DYSTROGLYCAN; DYSTROPHIN; GAMMA SARCOGLYCAN; SYNTROPHIN; UNCLASSIFIED DRUG; UTROPHIN;

ADOLESCENT; ADULT; AGED; ARTICLE; BECKER MUSCULAR DYSTROPHY; CHILD; CLINICAL ARTICLE; CYTOSKELETON; DISEASE CARRIER; DUCHENNE MUSCULAR DYSTROPHY; EXTRACELLULAR MATRIX; FEMALE; HUMAN; HUMAN CELL; IMMUNOBLOTTING; IMMUNOHISTOCHEMISTRY; MOSAICISM; MUSCLE CELL; PRIORITY JOURNAL; PROTEIN DEFECT; PROTEIN EXPRESSION; SYMPTOM;

ADOLESCENT; ADULT; AGED; CALCIUM-BINDING PROTEINS; CHILD; CHILD, PRESCHOOL; CYTOSKELETAL PROTEINS; DYSTROGLYCANS; DYSTROPHIN; DYSTROPHIN-ASSOCIATED PROTEINS; FEMALE; HETEROZYGOTE; HUMANS; IMMUNOBLOTTING; INFANT; MEMBRANE GLYCOPROTEINS; MEMBRANE PROTEINS; MUSCLE FIBERS; MUSCLE PROTEINS; MUSCULAR DYSTROPHIES; SARCOGLYCANS; UTROPHIN;

EID: 0029822953     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004010050532     Document Type: Article

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