High-level reconstitution of respiratory burst activity in a human X- linked chronic granulomatous disease (X-CGD) cell line and correction of murine X-CGD bone marrow cells by retroviral-mediated gene transfer of human gp91(phox)

Blood

Volumn 88, Issue 5, 1996, Pages 1834-1840

  Ding, Chunjin ^b   Kume, Akihiro ^b   Björgvinsdóttir, Helga ^b   Hawley, Robert G ^b   Pech, Nancy ^b   Dinauer, Mary C ^a  

^a RILEY HOSPITAL FOR CHILDREN   (United States)

^b NONE

Author keywords

[No Author keywords available]

Indexed keywords

CYTOCHROME B; MEMBRANE PROTEIN; OXIDOREDUCTASE;

ANIMAL CELL; ANTIMICROBIAL ACTIVITY; ARTICLE; BONE MARROW CELL; BONE MARROW CULTURE; CELL LINE; CHRONIC GRANULOMATOUS DISEASE; COLONY FORMING UNIT; ENZYME DEFECT; GENE MUTATION; GENE TRANSFER; GENETIC TRANSDUCTION; HUMAN; HUMAN CELL; MOUSE; NONHUMAN; PHAGOCYTE; PRIORITY JOURNAL; PROTEIN EXPRESSION; RESPIRATORY BURST; RETROVIRUS; X CHROMOSOME LINKAGE;

EID: 0029817964     PISSN: 00064971     EISSN: None     Source Type: Journal    
DOI: 10.1182/blood.v88.5.1834.1834     Document Type: Article

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