Coexistence of Huntington's disease and familial amyotrophic lateral sclerosis: Case presentation

Acta Neuropathologica

Volumn 92, Issue 4, 1996, Pages 421-427

  Rubio, A ^a   Steinberg, K ^a   Figlewicz, D A ^a   MacDonald, M E ^b   Greenamyre, T ^a,c   Hamill, R ^a,d   Shoulson, I ^a   Powers, J M ^a  

^a UNIVERSITY OF ROCHESTER MEDICAL CENTER   (United States)

^b MASSACHUSETTS GENERAL HOSPITAL   (United States)

^c EMORY UNIVERSITY SCHOOL OF MEDICINE   (United States)

^d UNIVERSITY OF VERMONT   (United States)

Author keywords

Amyotrophic lateral sclerosis; Heavy neurofilament subunit gene; Huntington's disease; Superoxide dismutase

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; TRINUCLEOTIDE; UBIQUITIN;

AGED; AGITATION; ALZHEIMER DISEASE; AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; AUTOPSY; BASAL GANGLION; BRAIN ATROPHY; BRAIN STEM; CASE REPORT; CELL LOSS; CHOREOATHETOSIS; CHROMOSOME 4P; CLINICAL FEATURE; COGNITIVE DEFECT; FAMILY HISTORY; GLIOSIS; HALLUCINATION; HUMAN; HUNTINGTON CHOREA; HYPOGLOSSAL NUCLEUS; MALE; MOLECULAR GENETICS; MOTONEURON; NEOCORTEX; NEOSTRIATUM; NERVE CELL; NEUROFILAMENT; NEUROPATHOLOGY; PERIKARYON; PERSONALITY DISORDER; PRIORITY JOURNAL; PYRAMIDAL TRACT; SPINAL CORD; SPINAL CORD VENTRAL HORN; SPINOCEREBELLAR TRACT;

AGED; AGED, 80 AND OVER; AMYOTROPHIC LATERAL SCLEROSIS; HUMANS; HUNTINGTON DISEASE; MALE; PEDIGREE;

EID: 0029816523     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004010050539     Document Type: Article

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