Mortality in patients with acute intermittent porphyria requiring hospitalization: A United States case series

American Journal of Medical Genetics

Volumn 65, Issue 4, 1996, Pages 269-273

  Jeans, Jennifer B ^a   Savik, Kay ^b   Gross, Cynthia R ^b   Weimer, Mary K ^a   Bossenmaier, Irene C ^a   Pierach, Claus A ^a   Bloomer, Joseph R ^a,c  

^a UNIVERSITY OF MINNESOTA   (United States)

^b UNIVERSITY OF MINNESOTA   (United States)

^c UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

Author keywords

acute intermittent porphyria; hematin; mortality; porphyric attack; prognosis

Indexed keywords

5 AMINOLEVULINATE SYNTHASE; HEMATIN; PORPHOBILINOGEN; PORPHOBILINOGEN DEAMINASE;

ABDOMINAL PAIN; ACUTE INTERMITTENT PORPHYRIA; ADOLESCENT; ADULT; AGED; ARTICLE; CONTROLLED STUDY; ENZYME ACTIVITY; FEMALE; HOSPITALIZATION; HUMAN; MAJOR CLINICAL STUDY; MALE; MORTALITY; NEUROLOGIC DISEASE; PRIORITY JOURNAL; PROGNOSIS; SCHOOL CHILD; SUICIDE; SURVIVAL RATE; UNITED STATES;

ADOLESCENT; ADULT; AGED; CHILD; FEMALE; HEMIN; HOSPITALS; HUMANS; MALE; MIDDLE AGED; PORPHYRIA, ACUTE INTERMITTENT; RECURRENCE; TREATMENT OUTCOME; UNITED STATES;

EID: 0029807940     PISSN: 01487299     EISSN: None     Source Type: Journal    
DOI: 10.1002/(SICI)1096-8628(19961111)65:4<269::AID-AJMG4>3.0.CO;2-K     Document Type: Article

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