-
1
-
-
0028157831
-
Localization of cystic fibrosis transmembrane conductance regulator mRNA in the human gastrointestinal tract by in situ hybridization
-
Strong TV, Boehm K, Collins FS: Localization of cystic fibrosis transmembrane conductance regulator mRNA in the human gastrointestinal tract by in situ hybridization. J Clin Invest 1994, 93:347-354. This paper deals with the location of CFTR to epithelial cells of the alimentary tract and contributes to the understanding of the altered CFTR function at different sites of the gastrointestinal tract in cystic fibrosis.
-
(1994)
J Clin Invest
, vol.93
, pp. 347-354
-
-
Strong, T.V.1
Boehm, K.2
Collins, F.S.3
-
2
-
-
0026523829
-
Cystic fibrosis: Molecular biology and therapeutic implications
-
Collins FS: Cystic fibrosis: molecular biology and therapeutic implications. Science 1992, 256:774-779. The book gives valuable information of the knowledge on nutritional and intestinal disorders in cystic fibrosis before the indentification of the CFTR gene.
-
(1992)
Science
, vol.256
, pp. 774-779
-
-
Collins, F.S.1
-
4
-
-
0025951832
-
Small intestinal abnormalities in cystic fibrosis patients
-
Eggermont E, De Boeck K: Small intestinal abnormalities in cystic fibrosis patients. Eur J Pediatr 1991, 150:824-828. The study gives direct evidence of the lowered chloride absorption in rectal epithelium.
-
(1991)
Eur J Pediatr
, vol.150
, pp. 824-828
-
-
Eggermont, E.1
De Boeck, K.2
-
5
-
-
0026738918
-
Relationship between intestinal function and chloride secretion in patients with cystic fibrosis
-
Sinaasappel M: Relationship between intestinal function and chloride secretion in patients with cystic fibrosis. Neth J Med 1992, 41:110-114.
-
(1992)
Neth J Med
, vol.41
, pp. 110-114
-
-
Sinaasappel, M.1
-
6
-
-
0026492809
-
Gastrointestinal complications in cystic fibrosis
-
Littlewood JM: Gastrointestinal complications in cystic fibrosis. Br Med Bull 1992, 48:847-859. Experimental data demonstrating that the clinical manifestations of cystic fibrosis can be found in CFTR (-/-) mice.
-
(1992)
Br Med Bull
, vol.48
, pp. 847-859
-
-
Littlewood, J.M.1
-
7
-
-
0026649122
-
An animal model for cystic fibrosis made by gene targeting
-
Snouwaert JN, Brigman KK, Latour AM, Malouf NN, Boucher RC, Smithies O, et al.: An animal model for cystic fibrosis made by gene targeting. Science 1992, 257:1083-1088.
-
(1992)
Science
, vol.257
, pp. 1083-1088
-
-
Snouwaert, J.N.1
Brigman, K.K.2
Latour, A.M.3
Malouf, N.N.4
Boucher, R.C.5
Smithies, O.6
-
8
-
-
9444250314
-
Pathology
-
Edited by Lloyd-Still JD. Boston: John Wright PSG Inc
-
Lloyd-Still JD: Pathology. In Textbook of Cystic Fibrosis. Edited by Lloyd-Still JD. Boston: John Wright PSG Inc; 1983:3.19-3.31.
-
(1983)
Textbook of Cystic Fibrosis
, pp. 319-331
-
-
Lloyd-Still, J.D.1
-
9
-
-
0039776844
-
Pancreatic function in disease in early life; pathological changes associated with pancreatic insufficiency in early life
-
Farber S: Pancreatic function in disease in early life; pathological changes associated with pancreatic insufficiency in early life. Arch Pathol (Chicago) 1944, 37:250-283.
-
(1944)
Arch Pathol (Chicago)
, vol.37
, pp. 250-283
-
-
Farber, S.1
-
10
-
-
0012743754
-
Submaxillary salivary enzymes as a measure of glandular activity in cystic fibrosis
-
Chernick WS, Eichel HJ, Barbero GJ: Submaxillary salivary enzymes as a measure of glandular activity in cystic fibrosis. J Pediatr 1964, 65:694-700.
-
(1964)
J Pediatr
, vol.65
, pp. 694-700
-
-
Chernick, W.S.1
Eichel, H.J.2
Barbero, G.J.3
-
11
-
-
0019219314
-
Lingual lipase: An important lipase in the digestion of dietary lipids in cystic fibrosis?
-
Fredrikzon B, Blackberg L: Lingual lipase: an important lipase in the digestion of dietary lipids in cystic fibrosis? Pediatr Res 1980, 14:1387-1390.
-
(1980)
Pediatr Res
, vol.14
, pp. 1387-1390
-
-
Fredrikzon, B.1
Blackberg, L.2
-
12
-
-
0020053409
-
Complications of gastroesophageal reflux in patients with cystic fibrosis
-
Bendig DW, Seilheimer DK, Wagner ML, Ferry GD, Harrison GM. Complications of gastroesophageal reflux in patients with cystic fibrosis. J Pediatr 1982, 100:536-540. Pathological gastrointestinal reflux is frequent in cystic fibrosis and is predominantly caused by the transient inappropriate lower oesophageal sphincter relaxation rather than a low steady state basal oesophageal sphincter pressure.
-
(1982)
J Pediatr
, vol.100
, pp. 536-540
-
-
Bendig, D.W.1
Seilheimer, D.K.2
Wagner, M.L.3
Ferry, G.D.4
Harrison, G.M.5
-
13
-
-
0025821810
-
Mechanisms of gastro-oesophageal reflux in cystic fibrosis
-
Cucchiara S, Santamaria F, Andreotti MR, Minella R, Ercolini P, Oggero V, et al.: Mechanisms of gastro-oesophageal reflux in cystic fibrosis. Arch Dis Child 1991, 66:617-622.
-
(1991)
Arch Dis Child
, vol.66
, pp. 617-622
-
-
Cucchiara, S.1
Santamaria, F.2
Andreotti, M.R.3
Minella, R.4
Ercolini, P.5
Oggero, V.6
-
14
-
-
0019273276
-
Chronic organo-axial twisting of the stomach in infants born prematurely and affected by chronic respiratory disease
-
Eggermont E, Devlieger H, Marchal G, Jaeken J, Vandevoorde P, Goddeeris P, et al.: Chronic organo-axial twisting of the stomach in infants born prematurely and affected by chronic respiratory disease. Acta Paediatr Belg 1980, 33:233-242.
-
(1980)
Acta Paediatr Belg
, vol.33
, pp. 233-242
-
-
Eggermont, E.1
Devlieger, H.2
Marchal, G.3
Jaeken, J.4
Vandevoorde, P.5
Goddeeris, P.6
-
15
-
-
0026048329
-
New insights on gastro-oesophageal reflux in cystic fibrosis by longitudinal follow-up
-
Malfroot A, Dab I: New insights on gastro-oesophageal reflux in cystic fibrosis by longitudinal follow-up. Arch Dis Child 1991, 66:1339-1345.
-
(1991)
Arch Dis Child
, vol.66
, pp. 1339-1345
-
-
Malfroot, A.1
Dab, I.2
-
16
-
-
0023248742
-
Comparison of gastrointestinal pH in cystic fibrosis and healthy subjects
-
Youngberg CA, Berardi RR, Howart WF, Hyneck ML, Amidon GL, Meyer JH, et al.: Comparison of gastrointestinal pH in cystic fibrosis and healthy subjects. Dig Dis Sci 1987, 32:472-480.
-
(1987)
Dig Dis Sci
, vol.32
, pp. 472-480
-
-
Youngberg, C.A.1
Berardi, R.R.2
Howart, W.F.3
Hyneck, M.L.4
Amidon, G.L.5
Meyer, J.H.6
-
17
-
-
0025681706
-
Lingual and gastric lipases
-
Hamosh M: Lingual and gastric lipases. Nutrition 1990, 6:421-428.
-
(1990)
Nutrition
, vol.6
, pp. 421-428
-
-
Hamosh, M.1
-
18
-
-
8044220950
-
Hypersecretion of gastric acid in patients with pancreatic exocrine insufficiency due to cystic fibrosis
-
Cox K, Isenberg JN: Hypersecretion of gastric acid in patients with pancreatic exocrine insufficiency due to cystic fibrosis. Gastroenterology 1978, 74:1022. Careful investigation of the effect of cystic fibrosis on plasma gut hormones. The postprandial hormonal response is similar to the findings in patietns with mucosal damage, e.g. coeliac disease.
-
(1978)
Gastroenterology
, vol.74
, pp. 1022
-
-
Cox, K.1
Isenberg, J.N.2
-
19
-
-
0018873104
-
Hormonal abnormalities of the pancreas and gut in cystic fibrosis
-
Adrian TE, McKiernan J, Johnstone DI, Miller EJ, Vyas H, Sarson DL, et al.: Hormonal abnormalities of the pancreas and gut in cystic fibrosis. Gastroenterology 1980, 79:460-465.
-
(1980)
Gastroenterology
, vol.79
, pp. 460-465
-
-
Adrian, T.E.1
McKiernan, J.2
Johnstone, D.I.3
Miller, E.J.4
Vyas, H.5
Sarson, D.L.6
-
20
-
-
0007856707
-
Gastrointestinal and pancreatic disease in cystic fibrosis
-
Edited by Hodson ME, Geddes DM. London: Chapman & Hall Medical
-
Davidson AGF: Gastrointestinal and pancreatic disease in cystic fibrosis. In Cystic Fibrosis. Edited by Hodson ME, Geddes DM. London: Chapman & Hall Medical; 1995:10.259-10.280.
-
(1995)
Cystic Fibrosis
, pp. 10259-10280
-
-
Davidson, A.G.F.1
-
21
-
-
0024453308
-
Identification of the cystic fibrosis gene: Chromosome walking and jumping
-
Rommens JM, Jannuzzi MC, Kerem BS, Drumm MR, Melmer G, Dean M, et al.: Identification of the cystic fibrosis gene: chromosome walking and jumping. Science 1989, 245:1059-1065.
-
(1989)
Science
, vol.245
, pp. 1059-1065
-
-
Rommens, J.M.1
Jannuzzi, M.C.2
Kerem, B.S.3
Drumm, M.R.4
Melmer, G.5
Dean, M.6
-
22
-
-
0024424270
-
Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA
-
Riordan JR, Rommens JM, Kerem BS, Alon N, Rozmahel R, Grzelczak Z, et al.: Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA. Science 1989, 245:1066-1073.
-
(1989)
Science
, vol.245
, pp. 1066-1073
-
-
Riordan, J.R.1
Rommens, J.M.2
Kerem, B.S.3
Alon, N.4
Rozmahel, R.5
Grzelczak, Z.6
-
23
-
-
0025868103
-
Demonstration that CFTR is a chloride channel by alteration of its anion selectivity
-
Anderson MP, Gregory RJ, Thompson S, Souza DW, Paul S, Mulligan RC, et al.: Demonstration that CFTR is a chloride channel by alteration of its anion selectivity. Science 1991, 253:202-205.
-
(1991)
Science
, vol.253
, pp. 202-205
-
-
Anderson, M.P.1
Gregory, R.J.2
Thompson, S.3
Souza, D.W.4
Paul, S.5
Mulligan, R.C.6
-
24
-
-
0026532895
-
Purification and functional reconstitution of the cystic fibrosis transmembrane conductance regulator (CFTR)
-
Bear CE, Li C, Kartner N, Bridges RJ, Jensen TJ, Ramjeesingh M, et al.: Purification and functional reconstitution of the cystic fibrosis transmembrane conductance regulator (CFTR). Cell 1992, 68:809-818.
-
(1992)
Cell
, vol.68
, pp. 809-818
-
-
Bear, C.E.1
Li, C.2
Kartner, N.3
Bridges, R.J.4
Jensen, T.J.5
Ramjeesingh, M.6
-
25
-
-
0026448462
-
Cystic fibrosis gene
-
Harris A: Cystic fibrosis gene. Br Med Bull 1992, 48:738-753.
-
(1992)
Br Med Bull
, vol.48
, pp. 738-753
-
-
Harris, A.1
-
26
-
-
0025349031
-
Cystic fibrosis: A disease in electrolyte transport
-
Quinton PM: Cystic fibrosis: a disease in electrolyte transport. FASEB J 1990, 4:2709-2717.
-
(1990)
FASEB J
, vol.4
, pp. 2709-2717
-
-
Quinton, P.M.1
-
27
-
-
0027207509
-
Expression of the cystic fibrosis gene in human foetal tissues
-
Trezise AEO, Chambers JA, Wardle CJ, Gould S, Harris A: Expression of the cystic fibrosis gene in human foetal tissues. Hum Mol Genet 1993, 2:213-218.
-
(1993)
Hum Mol Genet
, vol.2
, pp. 213-218
-
-
Trezise, A.E.O.1
Chambers, J.A.2
Wardle, C.J.3
Gould, S.4
Harris, A.5
-
28
-
-
0027195534
-
Cell-specific localization of CFTR mRNA shows developmentally regulated expression in human fetal tissues
-
Tizzano EF, Chitayat D, Buchwald M: Cell-specific localization of CFTR mRNA shows developmentally regulated expression in human fetal tissues. Hum Molec Gen 1993, 2:219-224. In vitro experiments show a 120-fold increase of CFTR mRNA of intestinal epithelial cells. The increase cannot be accounted for by increased transcription of the gene and suggests the presence of CFTR mRNA stabilizing factor(s).
-
(1993)
Hum Molec Gen
, vol.2
, pp. 219-224
-
-
Tizzano, E.F.1
Chitayat, D.2
Buchwald, M.3
-
29
-
-
0026751116
-
Regulation of CFTR expression and function during differentiation of intestinal epithelial cells
-
Sood R, Bear C, Auerbach W, Reyes E, Jensen T, Kartner N, et al.: Regulation of CFTR expression and function during differentiation of intestinal epithelial cells. EMBO J 1992, 11:2487-2494.
-
(1992)
EMBO J
, vol.11
, pp. 2487-2494
-
-
Sood, R.1
Bear, C.2
Auerbach, W.3
Reyes, E.4
Jensen, T.5
Kartner, N.6
-
30
-
-
0026451638
-
The multidrug resistance and cystic fibrosis genes have complementary patterns of epithelial expression
-
Trezise AEO, Romano PR, Gill DR, Hyde SC, Sepúlveda FV, Buchwald M, et al.: The multidrug resistance and cystic fibrosis genes have complementary patterns of epithelial expression. EMBO J 1992, 11:4291-4303.
-
(1992)
EMBO J
, vol.11
, pp. 4291-4303
-
-
Trezise, A.E.O.1
Romano, P.R.2
Gill, D.R.3
Hyde, S.C.4
Sepúlveda, F.V.5
Buchwald, M.6
-
31
-
-
0026582066
-
Quantitative expression patterns of multidrug-resistance P-glycoprotein (MDR1) and differentially spliced cystic-fibrosis transmembrane-conductance regulator mRNA transcripts in human epithelia
-
Bremer S, Hoof T, Wilke M, Busche R, Scholte B, Riordan JR, et al.: Quantitative expression patterns of multidrug-resistance P-glycoprotein (MDR1) and differentially spliced cystic-fibrosis transmembrane-conductance regulator mRNA transcripts in human epithelia. Eur J Biochem 1992, 206:137-149.
-
(1992)
Eur J Biochem
, vol.206
, pp. 137-149
-
-
Bremer, S.1
Hoof, T.2
Wilke, M.3
Busche, R.4
Scholte, B.5
Riordan, J.R.6
-
32
-
-
0025784535
-
Defective acidification of intracellular organelles in cystic fibrosis
-
Barasch J, Kiss B, Prince A, Saiman L, Gruenert D, Al-Awqati Q: Defective acidification of intracellular organelles in cystic fibrosis. Nature 1991, 352:70-73. Examination of mutant CFTR shows an incomplete version of the proteins in the endoplasmic reticulum and the absence of mature CFTR at the correct brush border locaiton.
-
(1991)
Nature
, vol.352
, pp. 70-73
-
-
Barasch, J.1
Kiss, B.2
Prince, A.3
Saiman, L.4
Gruenert, D.5
Al-Awqati, Q.6
-
33
-
-
0025242929
-
Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis
-
Cheng SH, Gregory RJ, Marshall J, Paul S, Souza DW, White GA, et al.: Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis. Cell 1990, 63:827-834.
-
(1990)
Cell
, vol.63
, pp. 827-834
-
-
Cheng, S.H.1
Gregory, R.J.2
Marshall, J.3
Paul, S.4
Souza, D.W.5
White, G.A.6
-
34
-
-
0021780659
-
The role of the small intestine in cystic fibrosis patients
-
Eggermont E: The role of the small intestine in cystic fibrosis patients. Acta Paediatr Scand 1985, suppl. 317:16-21.
-
(1985)
Acta Paediatr Scand
, Issue.317 SUPPL.
, pp. 16-21
-
-
Eggermont, E.1
-
35
-
-
0021249098
-
Fetal abnormalities in cystic fibrosis suggest a deficiency in proteolysis of cholecystokinin
-
Gosden CM, Gosden JR: Fetal abnormalities in cystic fibrosis suggest a deficiency in proteolysis of cholecystokinin. Lancet 1984, ii:541-546.
-
(1984)
Lancet
, vol.2
, pp. 541-546
-
-
Gosden, C.M.1
Gosden, J.R.2
-
36
-
-
0020666671
-
Human intestinal mucin in cystic fibrosis
-
Wesley A, Forstner J, Quershi R, Mantle M, Forstner G: Human intestinal mucin in cystic fibrosis. Pediatr Res 1983, 17:65-69.
-
(1983)
Pediatr Res
, vol.17
, pp. 65-69
-
-
Wesley, A.1
Forstner, J.2
Quershi, R.3
Mantle, M.4
Forstner, G.5
-
37
-
-
0025936105
-
MUC-2 human small intestinal mucin gene structure
-
Toribara NW, Gum JR, Culhane PJ, Lagace RE, Hicks JW, Petersen GM, et al.: MUC-2 human small intestinal mucin gene structure. J Clin Invest 1991, 88:1005-1013.
-
(1991)
J Clin Invest
, vol.88
, pp. 1005-1013
-
-
Toribara, N.W.1
Gum, J.R.2
Culhane, P.J.3
Lagace, R.E.4
Hicks, J.W.5
Petersen, G.M.6
-
38
-
-
0024591271
-
Intestinal mucins from normal subjects and patients with cystic fibrosis
-
Mantle M, Stewart G: Intestinal mucins from normal subjects and patients with cystic fibrosis. Biochem J 1989, 259:243-253. Biochemical studies of the intestinal mucins suggest that the three-dimensional conformation of CF mucins differ from that of normal mucus, leading to increased antigenicity.
-
(1989)
Biochem J
, vol.259
, pp. 243-253
-
-
Mantle, M.1
Stewart, G.2
-
39
-
-
0014469601
-
Disaccharides and cystic fibrosis of the pancreas
-
Gibbons ISE: Disaccharides and cystic fibrosis of the pancreas. Arch Dis Child 1969, 44:63-68.
-
(1969)
Arch Dis Child
, vol.44
, pp. 63-68
-
-
Gibbons, I.S.E.1
-
40
-
-
0025315706
-
Small intestinal permeability and orocaecal transit time in cystic fibrosis
-
Dalzell AM, Freestone NS, Billington D, Heaf DP: Small intestinal permeability and orocaecal transit time in cystic fibrosis. Arch Dis Child 1990, 65:585-588.
-
(1990)
Arch Dis Child
, vol.65
, pp. 585-588
-
-
Dalzell, A.M.1
Freestone, N.S.2
Billington, D.3
Heaf, D.P.4
-
41
-
-
0242328302
-
Intestinal permeability in children with cystic fibrosis: Lactulose/mannitol, lactulose/creatinine and mannitol/creatinine excretion ratios
-
Sierra C, Valverde E, Ortega C, Picazo B, Martínez A, Sánchez-Font E: Intestinal permeability in children with cystic fibrosis: lactulose/mannitol, lactulose/creatinine and mannitol/creatinine excretion ratios. J Clin Nutr Gastroenterol 1993, 8:94-99.
-
(1993)
J Clin Nutr Gastroenterol
, vol.8
, pp. 94-99
-
-
Sierra, C.1
Valverde, E.2
Ortega, C.3
Picazo, B.4
Martínez, A.5
Sánchez-Font, E.6
-
43
-
-
0026598097
-
Correlation of intestinal lactulose permeability with exocrine pancreatic dysfunction
-
Mack DR, Flick JA, Durie PR, Rosenstein BJ, Ellis LE, Perman JA: Correlation of intestinal lactulose permeability with exocrine pancreatic dysfunction. J Pediatr 1992, 120:697-701.
-
(1992)
J Pediatr
, vol.120
, pp. 697-701
-
-
Mack, D.R.1
Flick, J.A.2
Durie, P.R.3
Rosenstein, B.J.4
Ellis, L.E.5
Perman, J.A.6
-
44
-
-
0004994139
-
Studies on meconium
-
Edited by Lebenthal E. New York: Raven Press
-
Shwachman H, Antonowicz I: Studies on meconium. In Textbook of Gastroenterology and Nutrition in Infancy. Edited by Lebenthal E. New York: Raven Press; 1981:9.83-9.93. This paper dererves special attention becuase it is written by the pioneers of the study of gastrointestinal dysfunction in cystic fibrosis.
-
(1981)
Textbook of Gastroenterology and Nutrition in Infancy
, pp. 983-993
-
-
Shwachman, H.1
Antonowicz, I.2
-
45
-
-
0016826054
-
Une anomalie coprologique dans la mucoviscidose
-
Pecau Y, Feigelson J: Une anomalie coprologique dans la mucoviscidose. Arch Fr Pédiatr 1975, 32:733-740.
-
(1975)
Arch Fr Pédiatr
, vol.32
, pp. 733-740
-
-
Pecau, Y.1
Feigelson, J.2
-
46
-
-
0019441929
-
Gastrointestinal manifestations of cystic fibrosis - A review
-
Park RW, Grand RJ: Gastrointestinal manifestations of cystic fibrosis - a review. Gastroenterology 1981, 81:1143-1161.
-
(1981)
Gastroenterology
, vol.81
, pp. 1143-1161
-
-
Park, R.W.1
Grand, R.J.2
-
47
-
-
9444272057
-
Alpha-1-antitrypsin clearance in children with cystic fibrosis
-
Wulkan RW, Sinaasappel M, Bouquet J, Lindemans J: Alpha-1-antitrypsin clearance in children with cystic fibrosis. Pediatr Pulmonol 1990, 9(suppl. 5):272.
-
(1990)
Pediatr Pulmonol
, vol.9
, Issue.5 SUPPL.
, pp. 272
-
-
Wulkan, R.W.1
Sinaasappel, M.2
Bouquet, J.3
Lindemans, J.4
-
48
-
-
0023730817
-
Failure to induce secretion in jejunal biopsies from children with cystic fibrosis
-
Taylor CJ, Baxter PS, Hardcastle J, Hardcastle PT: Failure to induce secretion in jejunal biopsies from children with cystic fibrosis. Gut 1988, 29:957-962.
-
(1988)
Gut
, vol.29
, pp. 957-962
-
-
Taylor, C.J.1
Baxter, P.S.2
Hardcastle, J.3
Hardcastle, P.T.4
-
49
-
-
0028062781
-
Cystic fibrosis heterozygote resistance to cholera toxin in the cystic fibrosis mouse model
-
Gabriel SE, Brigman KN, Koller BA, Boucher RC, Stutts MJ: Cystic fibrosis heterozygote resistance to cholera toxin in the cystic fibrosis mouse model. Science 1994, 266:107-109.
-
(1994)
Science
, vol.266
, pp. 107-109
-
-
Gabriel, S.E.1
Brigman, K.N.2
Koller, B.A.3
Boucher, R.C.4
Stutts, M.J.5
-
51
-
-
0345012686
-
Disaccharidase activities in pancreatic insufficiency and reappraisal of lactase activity in cystic fibrosis
-
Antonowicz I, Lebenthal E, Shwachman H: Disaccharidase activities in pancreatic insufficiency and reappraisal of lactase activity in cystic fibrosis. Pediatr Res 1976, 10:351.
-
(1976)
Pediatr Res
, vol.10
, pp. 351
-
-
Antonowicz, I.1
Lebenthal, E.2
Shwachman, H.3
-
53
-
-
0022007108
-
Enhanced glucose absorption in the jejunum of patients with cystic fibrosis
-
Frase LL, Strickland AD, Kachel GW, Krejs GJ: Enhanced glucose absorption in the jejunum of patients with cystic fibrosis. Gastroenterology 1985, 88:478-484.
-
(1985)
Gastroenterology
, vol.88
, pp. 478-484
-
-
Frase, L.L.1
Strickland, A.D.2
Kachel, G.W.3
Krejs, G.J.4
-
54
-
-
0025300405
-
Enhanced intestinal glucose and alanine transport in cystic fibrosis
-
Baxter P, Goldhill J, Hardcastle J, Hardcastle PT, Taylor CJ: Enhanced intestinal glucose and alanine transport in cystic fibrosis. Gut 1990, 31:817-820.
-
(1990)
Gut
, vol.31
, pp. 817-820
-
-
Baxter, P.1
Goldhill, J.2
Hardcastle, J.3
Hardcastle, P.T.4
Taylor, C.J.5
-
55
-
-
0028121126
-
Loperamide inhibits the enhanced intestinal glucose absorption of cystic fibrosis in vitro
-
Hardcastle J, Hardcastle PT, Taylor CJ: Loperamide inhibits the enhanced intestinal glucose absorption of cystic fibrosis in vitro. Pediatr Res 1994, 35:354-356.
-
(1994)
Pediatr Res
, vol.35
, pp. 354-356
-
-
Hardcastle, J.1
Hardcastle, P.T.2
Taylor, C.J.3
-
56
-
-
0020056746
-
Intestinal bile acid malabsorption in cystic fibrosis: A primary mucosal cell defect
-
Fondacaro JD, Heubi JE, Kellog FW: Intestinal bile acid malabsorption in cystic fibrosis: a primary mucosal cell defect. Pediatr Res 1982, 16:494-498.
-
(1982)
Pediatr Res
, vol.16
, pp. 494-498
-
-
Fondacaro, J.D.1
Heubi, J.E.2
Kellog, F.W.3
-
57
-
-
0023851546
-
In vivo bile acid uptake from terminal ileum in cystic fibrosis
-
Thompson GN, Davidson GP: In vivo bile acid uptake from terminal ileum in cystic fibrosis. Pediatr Res 1988, 23:323-328.
-
(1988)
Pediatr Res
, vol.23
, pp. 323-328
-
-
Thompson, G.N.1
Davidson, G.P.2
-
58
-
-
0022633576
-
Chronic undernutrition/growth retardation in cystic fibrosis
-
Soutter VL, Kristidis P, Gruca MA, Gaskin KJ: Chronic undernutrition/growth retardation in cystic fibrosis. Clin Gastroenterol 1986, 15:137-155.
-
(1986)
Clin Gastroenterol
, vol.15
, pp. 137-155
-
-
Soutter, V.L.1
Kristidis, P.2
Gruca, M.A.3
Gaskin, K.J.4
-
59
-
-
0025772974
-
Ion transport abnormalities in rectal suction biopsies from children with cystic fibrosis
-
Veeze HJ, Sinaasappel M, Bijman J, Bouquet J, De Jonge HR: Ion transport abnormalities in rectal suction biopsies from children with cystic fibrosis. Gastroenterology 1991, 101:398-403. The short-circuit current response to specific stimuli of both cyclic adenosine monophosphate and calcium-mediated chloride transport is drastically altered in all cystic fibrosis rectal biopsy specimens. Since, it has become a valuable criterion to diagnose cystic fibrosis for those patients in whom the sweat test and DNA analysis are inconclusive.
-
(1991)
Gastroenterology
, vol.101
, pp. 398-403
-
-
Veeze, H.J.1
Sinaasappel, M.2
Bijman, J.3
Bouquet, J.4
De Jonge, H.R.5
-
60
-
-
0025776179
-
Failure of cholinergic stimulation to induce a secretory response from the rectal mucosa in cystic fibrosis
-
Hardcastle J, Hardcastle PT, Taylor CJ, Goldhill J: Failure of cholinergic stimulation to induce a secretory response from the rectal mucosa in cystic fibrosis. Gut 1991, 32:1035-1039.
-
(1991)
Gut
, vol.32
, pp. 1035-1039
-
-
Hardcastle, J.1
Hardcastle, P.T.2
Taylor, C.J.3
Goldhill, J.4
-
61
-
-
0000204556
-
Studies in cystic fibrosis of the pancreas: Occurrence of rectal prolapse
-
Kulczycki LL, Shwachman H: Studies in cystic fibrosis of the pancreas: occurrence of rectal prolapse. N Engl J Med 1958, 259:409-412.
-
(1958)
N Engl J Med
, vol.259
, pp. 409-412
-
-
Kulczycki, L.L.1
Shwachman, H.2
-
62
-
-
0020062004
-
Treatment and prognosis of rectal prolapse in cystic fibrosis
-
Stern R, Izant RJ, Boat TF, Wood RE, Matthews LW, Doershuk CF: Treatment and prognosis of rectal prolapse in cystic fibrosis. Gastroenterology 1986, 82:707-710.
-
(1986)
Gastroenterology
, vol.82
, pp. 707-710
-
-
Stern, R.1
Izant, R.J.2
Boat, T.F.3
Wood, R.E.4
Matthews, L.W.5
Doershuk, C.F.6
-
63
-
-
9444297128
-
De appendix bij Mucoviscidose
-
Van der Steen K, Martens M, De Boeck K, Eggermont E, Geboes K: De appendix bij Mucoviscidose. Tijdschr voor Geneeskunde 1992, 48:613-616.
-
(1992)
Tijdschr Voor Geneeskunde
, vol.48
, pp. 613-616
-
-
Van Der Steen, K.1
Martens, M.2
De Boeck, K.3
Eggermont, E.4
Geboes, K.5
-
64
-
-
0026576213
-
A light lower quadrant mass in cystic fibrosis: A diagnostic challenge
-
Martens M, De Boeck K, Van der Steen K, Smet M, Eggermont E: A light lower quadrant mass in cystic fibrosis: a diagnostic challenge. Eur J Pediatr 1992, 151:329-331.
-
(1992)
Eur J Pediatr
, vol.151
, pp. 329-331
-
-
Martens, M.1
De Boeck, K.2
Van Der Steen, K.3
Smet, M.4
Eggermont, E.5
-
65
-
-
0025007051
-
Intussusception of the appendix in a patient with cystic fibrosis
-
McIntosh JC, Mroczek EC, Baldwin C, Mestre J: Intussusception of the appendix in a patient with cystic fibrosis. J Pediatr Gastroenterol Nutr 1990, 11:542-544.
-
(1990)
J Pediatr Gastroenterol Nutr
, vol.11
, pp. 542-544
-
-
McIntosh, J.C.1
Mroczek, E.C.2
Baldwin, C.3
Mestre, J.4
-
66
-
-
0028140481
-
Strictures of ascending colon in cystic fibrosis and high-strength pancreatic enzymes
-
Smyth RL, van Veizen D, Smyth AR, Lloyd DA, Heaf DP: Strictures of ascending colon in cystic fibrosis and high-strength pancreatic enzymes. Lancet 1994, 343:85-86.
-
(1994)
Lancet
, vol.343
, pp. 85-86
-
-
Smyth, R.L.1
Van Veizen, D.2
Smyth, A.R.3
Lloyd, D.A.4
Heaf, D.P.5
-
67
-
-
23444436250
-
Colonic strictures in cystic fibrosis
-
Taylor CJ: Colonic strictures in cystic fibrosis. Lancet 1994, 343:615-616.
-
(1994)
Lancet
, vol.343
, pp. 615-616
-
-
Taylor, C.J.1
-
68
-
-
0028152828
-
Pancolonic disease in cystic fibrosis and high-dose pancreatic enzyme therapy
-
Pettei MT, Leonidas JC, Levine JJ, Gorvoy JD: Pancolonic disease in cystic fibrosis and high-dose pancreatic enzyme therapy. J Pediatr 1994, 125:587-589. First report warning clinicians that high-dose pancreatic enzyme therapy is not always beneficial to cystic fibrosis patients.
-
(1994)
J Pediatr
, vol.125
, pp. 587-589
-
-
Pettei, M.T.1
Leonidas, J.C.2
Levine, J.J.3
Gorvoy, J.D.4
-
69
-
-
0021713404
-
A rational approach to meeting macro- and micronutrient needs in cystic fibrosis
-
Roy CC, Darling P, Weber AM: A rational approach to meeting macro- and micronutrient needs in cystic fibrosis. J Pediatr Gastroenterol Nutr 1984, 3(suppl. 1):S154-S162.
-
(1984)
J Pediatr Gastroenterol Nutr
, vol.3
, Issue.1 SUPPL.
-
-
Roy, C.C.1
Darling, P.2
Weber, A.M.3
-
70
-
-
0026541404
-
Nutritional assessment and management of cystic fibrosis: A consensus report
-
Ramsey BW, Farrell PM, Pencharz P and the Consensus Committee: Nutritional assessment and management of cystic fibrosis: a consensus report. Am J Clin Nutr 1992, 55:108-116.
-
(1992)
Am J Clin Nutr
, vol.55
, pp. 108-116
-
-
Ramsey, B.W.1
Farrell, P.M.2
Pencharz, P.3
-
71
-
-
0029012022
-
Nutritional management of the infant with cystic fibrosis
-
Green MR, Buchanan E, Weaver LT: Nutritional management of the infant with cystic fibrosis. Arch Dis Child 1995, 72:452-456.
-
(1995)
Arch Dis Child
, vol.72
, pp. 452-456
-
-
Green, M.R.1
Buchanan, E.2
Weaver, L.T.3
-
72
-
-
0025237250
-
Human pancreatic secretion and intestinal motility: Effects of ileal nutrient perfusion
-
Layer P, Peschel S, Schlesinger T, Goebell H: Human pancreatic secretion and intestinal motility: effects of ileal nutrient perfusion. Am J Physiol 1990, 258:G196-G201.
-
(1990)
Am J Physiol
, vol.258
-
-
Layer, P.1
Peschel, S.2
Schlesinger, T.3
Goebell, H.4
-
73
-
-
0029054666
-
Faecal interleukin-8 and tumour necrosing factor-alfa concentrations in cystic fibrosis
-
Briars GL, Dean TP, Murphy JL, Rolles CJ, Warner JO: Faecal interleukin-8 and tumour necrosing factor-alfa concentrations in cystic fibrosis. Arch Dis Child 1995, 73:74-76.
-
(1995)
Arch Dis Child
, vol.73
, pp. 74-76
-
-
Briars, G.L.1
Dean, T.P.2
Murphy, J.L.3
Rolles, C.J.4
Warner, J.O.5
-
74
-
-
0014428204
-
Pancreozymin secretion test of exocrine pancreatic function in cystic fibrosis and the significance of the result for the pathogenesis of the disease
-
Hadorn B, Johansen PG, Anderson CM: Pancreozymin secretion test of exocrine pancreatic function in cystic fibrosis and the significance of the result for the pathogenesis of the disease. Can Med Ass J 1968, 98:377-385. This is still the leading paper for the study of pancreatic exocrine function in normal and cystic fibrosis patients.
-
(1968)
Can Med Ass J
, vol.98
, pp. 377-385
-
-
Hadorn, B.1
Johansen, P.G.2
Anderson, C.M.3
-
75
-
-
0021369735
-
Colipase and lipase secretion in childhood-onset pancreatic insufficiency
-
Gaskin KJ, Durie PR, Hill R, Forstner GG: Colipase and lipase secretion in childhood-onset pancreatic insufficiency. Gastroenterology 1984, 86:1-7.
-
(1984)
Gastroenterology
, vol.86
, pp. 1-7
-
-
Gaskin, K.J.1
Durie, P.R.2
Hill, R.3
Forstner, G.G.4
-
76
-
-
0021338655
-
Effect of intrajejunal acidity on aqueous phase bile acid and lipid concentrations in pancreatic steatorrhoea due to cystic fibrosis
-
Zentler-Munro PL, Fitzpatrick WJF, Batten JC, Northfield TC: Effect of intrajejunal acidity on aqueous phase bile acid and lipid concentrations in pancreatic steatorrhoea due to cystic fibrosis. Gut 1984, 25:500-507.
-
(1984)
Gut
, vol.25
, pp. 500-507
-
-
Zentler-Munro, P.L.1
Fitzpatrick, W.J.F.2
Batten, J.C.3
Northfield, T.C.4
-
77
-
-
0028909863
-
Liver disease in cystic fibrosis
-
Tanner MS, Taylor CJ: Liver disease in cystic fibrosis. Arch Dis Child 1995, 72:281-284.
-
(1995)
Arch Dis Child
, vol.72
, pp. 281-284
-
-
Tanner, M.S.1
Taylor, C.J.2
-
78
-
-
0019404760
-
Comparative study of varying regimes to improve steatorrhoea and creatorrhoea in cystic fibrosis: Effectiveness of an enteric-coated preparation with and without antacids and cimetidine
-
Gow R, Francis P, Bradbear R, Shepherd R: Comparative study of varying regimes to improve steatorrhoea and creatorrhoea in cystic fibrosis: effectiveness of an enteric-coated preparation with and without antacids and cimetidine. Lancet 1981, ii:1071-1074.
-
(1981)
Lancet
, vol.2
, pp. 1071-1074
-
-
Gow, R.1
Francis, P.2
Bradbear, R.3
Shepherd, R.4
-
79
-
-
0023248742
-
Comparison of gastrointestinal pH in cystic fibrosis and healthy subjects
-
Youngberg CA, Berardi RR, Howatt WF, Hyneck ML, Amidon GL, Meyer JH, et al.: Comparison of gastrointestinal pH in cystic fibrosis and healthy subjects. Dig Dis Sci 1987, 32:472-480.
-
(1987)
Dig Dis Sci
, vol.32
, pp. 472-480
-
-
Youngberg, C.A.1
Berardi, R.R.2
Howatt, W.F.3
Hyneck, M.L.4
Amidon, G.L.5
Meyer, J.H.6
-
80
-
-
0023803911
-
Ileal pH in cystic fibrosis
-
Gilbert J, Kelleher J, Littlewood JM, Evans DF: Ileal pH in cystic fibrosis. Scand J Gastroenterol 1988, 23(suppl. 143):132-134.
-
(1988)
Scand J Gastroenterol
, vol.23
, Issue.143 SUPPL.
, pp. 132-134
-
-
Gilbert, J.1
Kelleher, J.2
Littlewood, J.M.3
Evans, D.F.4
-
81
-
-
0021741710
-
Abnormal mucus: Nominated but not yet elected
-
Forstner J, Wesley A, Mantle M, Koppelman H, Man D, Forstner G: Abnormal mucus: nominated but not yet elected. J Pediatr Gastroenterol Nutr 1984, 3(suppl. 1):S67-S73.
-
(1984)
J Pediatr Gastroenterol Nutr
, vol.3
, Issue.1 SUPPL.
-
-
Forstner, J.1
Wesley, A.2
Mantle, M.3
Koppelman, H.4
Man, D.5
Forstner, G.6
-
82
-
-
0024114009
-
Pancreatic function testing in meconium disease in cystic fibrosis
-
Eggermont E: Pancreatic function testing in meconium disease in cystic fibrosis. J Pediatr Gastroenterol Nutr 1988, 7:935.
-
(1988)
J Pediatr Gastroenterol Nutr
, vol.7
, pp. 935
-
-
Eggermont, E.1
-
83
-
-
0025364793
-
Excessive faecal losses of vitamin A (retinol) in cystic fibrosis
-
Ahmed F, Ellis J, Murphy J, Wootton S, Jackson AA: Excessive faecal losses of vitamin A (retinol) in cystic fibrosis. Arch Dis Child 1990, 65:589-593.
-
(1990)
Arch Dis Child
, vol.65
, pp. 589-593
-
-
Ahmed, F.1
Ellis, J.2
Murphy, J.3
Wootton, S.4
Jackson, A.A.5
-
84
-
-
0022921801
-
Intestinal retinol esterification and serum retinol in children with cystic fibrosis
-
Rasmussen M, Michalsen H, Lie SO, Nilsson A, Petersen LB, Norum KR: Intestinal retinol esterification and serum retinol in children with cystic fibrosis. J Pediatr Gastroenterol 1986, 5:397-403.
-
(1986)
J Pediatr Gastroenterol
, vol.5
, pp. 397-403
-
-
Rasmussen, M.1
Michalsen, H.2
Lie, S.O.3
Nilsson, A.4
Petersen, L.B.5
Norum, K.R.6
|