Hb Montefiore (α126(H9)Asp → Tyr). High oxygen affinity and loss of cooperativity secondary to C-terminal disruption

Journal of Biological Chemistry

Volumn 271, Issue 38, 1996, Pages 22990-22998

  Wajcman, Henri ^a   Kister, Jean ^b   Galactéros, Frédèric ^a   Spielvogel, Arthur ^c   Lin, Margaret J ^c   Vidugiris, Gediminas J A ^c,d   Hirsch, Rhoda Elison ^c   Friedman, Joel M ^d   Nagel, Ronald L ^c,d  

^a HENRI MONDOR HOSPITAL   (France)

^b BICÊTRE HOSPITAL   (France)

^c MONTEFIORE MEDICAL CENTER   (United States)

^d ALBERT EINSTEIN COLLEGE OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

2,3 DIPHOSPHOGLYCERIC ACID; HEMOGLOBIN; HEMOGLOBIN MONTEFIORE; PHYTIC ACID; UNCLASSIFIED DRUG; ASPARTIC ACID; HEMOGLOBIN VARIANT; OXYGEN; TYROSINE;

ARTICLE; CASE REPORT; FEMALE; FLUORESCENCE; HEMOGLOBIN ANALYSIS; HEMOGLOBIN DETERMINATION; HUMAN; OXYGEN AFFINITY; PRIORITY JOURNAL; PROTEIN BINDING; SPECTROSCOPY; STRUCTURE ACTIVITY RELATION; STRUCTURE ANALYSIS; ALLOSTERISM; CHEMISTRY; ERYTHROCYTE; ETHNOLOGY; GENETICS; HETEROZYGOTE; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; METABOLISM; MUTATION; NEWBORN; PUERTO RICO; RAMAN SPECTROMETRY; SPECTROFLUOROMETRY;

ALLOSTERIC REGULATION; ASPARTIC ACID; CHROMATOGRAPHY, HIGH PRESSURE LIQUID; ERYTHROCYTES; FEMALE; HEMOGLOBINS, ABNORMAL; HETEROZYGOTE; HUMANS; INFANT, NEWBORN; MUTATION; OXYGEN; PUERTO RICO; SPECTROMETRY, FLUORESCENCE; SPECTRUM ANALYSIS, RAMAN; TYROSINE;

EID: 0029661440     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.271.38.22990     Document Type: Article

References (28)

1. Balwin, J. M. (1976) Br. Med. Bull.32, 213-218
2. Lacombe, C., Riou, J., Godard, C., Rosa, J., and Galacteros, F. (1986) Acta Haematol.78, 119-122
3. Schneider, R. G., and Barwick, R. C. (1986) in CRC Handbook Series in Clinical Laboratory Science, Section1: Hematology (Schmidt, R. M., and Fairbanks, V. F., eds) Vol IV, pp. 125-139, CRC Press, Boca Raton, FL
4. Radola, B. J. (1973) N. Y. Acad. Sci.209, 127-143
5. Wajcman, H., Bardakdjian, J., and Ducrocq, R. (1993) Ann. Biol. Clin.50, 867-870
6. Kister, J., Poyart, C., and Edelstein, S. J. (1987) J. Biol. Chem.252, 12085-12090
7. Monod, J., Wyman, J., and Changeux, J. P. (1967) J. Mol. Biol.12, 88-118
8. Lalezari, I., Lalezari, P., Poyart, C., Marden, M., Kister, J., Bohn, B., Fermi, G., and Perutz, M. F. (1990) Biochemistry29, 1515-1523
9. Schroeder, W. A., and Huisman, T. H. J. (1980) Clinical and Biochemical Analysis, Vol.9, Marcel Dekker, Inc., New York
10. Hirsch, R. E. (1994) Methods Enzymol.232, 231-246
11. Eisinger, J. (1969) Biochemistry8, 3902-3907
12. Friedman, J. M., Stepnoski, R. A., Stavola, M., Ondrias, M. R., and Cone, R. L. (1982) Biochemistry21, 2022-2028
13. Rousseau, D. L., and Friedman, J. M. (1988) in Biological Application of Roman Spectroscopy (Spiro, T. G., ed) Vol. III, pp.133-215, John Wiley & Sons, New York
14. Perutz, M. F., Shih, D. T., and Williamson, D. (1994) J. Mol. Biol.239, 555-560
15. Findsen, E. W., Friedman, J. M., Ondrias, M. R., and Simon, S. R. (1985) Science229, 661-665
16. Scott, T. W., and Friedman, J. M. (1984) J. Am. Chem. Soc.106, 5677-5687
17. Jayaraman, V., Rodgers, K. R., Mukerji, I., and Spiro, T. G. (1995) Science269, 1843
18. Friedman, J. M. (1985) Science228, 1273-1280
19. Argade, P. V., Sassaroli, M., Rousseau, D. L., Inubushi, T., Ikeda-Saito, M., and Lapidot, R. (1984) J. Am. Chem. Soc.106, 6593-6596
20. Nagai, K., and Kitagawa, T. (1979) Proc. Natl. Acad. Sci. U. S. A.77, 2033-2037
21. Ondrias, M. R., Rousseau, D. L., Kitagawa, T., Ikeda-Saito, M., Inubushi, T., and Yonetani, T. (1982) J. Biol. Chem.257, 8766-8770
22. Friedman, J. M. (1994) Methods Enzymol.232, 205-231
23. Friedman, J. M., Rousseau, D. L., Ondrias, M. R., and Stepnoski, R. A. (1982) Science218, 1244-1246
24. Perutz, M. F., Fermi, G., Luisi, B., Shaanan, C., and Liddington, R. C. (1987) Acc. Chem. Res.20, 309-321
25. Stavroy, S. S. (1993) Biophys. J.65, 1942-1950
26. Pulsinelli, P. D. (1973) J. Mol. Biol.74, 57-66
27. Matsukawa, S., Mawatari, K., Yoneyama, Y., and Kitagawa, T. (1984) J. Am. Chem. Soc.107, 1108-1116
28. Fujii, M., Hori, H., Miyazaki, G., Morimoto, H., and Yonetani, T. (1993) J. Biol. Chem.268, 15386-15393