In vivo oxidation of [13C]galactose in patients with galactose-1- phosphate uridyltransferase deficiency

Biochemical and Molecular Medicine

Volumn 56, Issue 2, 1995, Pages 158-165

  Berry, Gerard T ^a   Nissim, Itzhak ^a   Mazur, Alice T ^a   Elsas, Louis J ^b   Singh, Rani H ^b   Klein, Peter D ^c   Gibson, James B ^a   Lin, Zhiping ^a   Segal, Stanton ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b EMORY UNIVERSITY   (United States)

^c U S DEPARTMENT OF AGRICULTURE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CARBON; GALACTOSE; GALACTOSE 1 PHOSPHATE URIDYLYLTRANSFERASE; GLUCOSE;

ADOLESCENT; ADULT; ARTICLE; BIOSYNTHESIS; BREATH ANALYSIS; CHILD; DISORDERS OF CARBOHYDRATE METABOLISM; FEMALE; GENETICS; HUMAN; MALE; MASS SPECTROMETRY; METABOLISM; MUTATION; REPRODUCIBILITY;

ADOLESCENT; ADULT; BREATH TESTS; CARBOHYDRATE METABOLISM, INBORN ERRORS; CARBON ISOTOPES; CHILD; FEMALE; GALACTOSE; GLUCOSE; HUMANS; MALE; MASS SPECTROMETRY; MUTATION; REPRODUCIBILITY OF RESULTS; UTP-HEXOSE-1-PHOSPHATE URIDYLYLTRANSFERASE;

EID: 0029414779     PISSN: 10773150     EISSN: None     Source Type: Journal    
DOI: 10.1006/bmme.1995.1071     Document Type: Article

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