An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria

Neuron

Volumn 14, Issue 6, 1995, Pages 1105-1116

  Wong, Philip C ^a   Pardo, Carlos A ^a   Borchelt, David R ^a   Lee, Michael K ^a   Copeland, Neal G ^b   Jenkins, Nancy A ^b   Sisodia, Sangram S ^a   Cleveland, Don W ^a,c   Price, Donald L ^a  

^a JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b Department of Biological Chemistry Johns Hopkins University School of Medicine Baltimore ^*  (United States)

^c UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL TISSUE; ARTICLE; BRAIN MITOCHONDRION; DENDRITE; ENZYME ACTIVITY; MOTOR NEURON DISEASE; MOUSE; NERVE FIBER; NEUROFILAMENT; NONHUMAN; PRIORITY JOURNAL; PROTEIN FOLDING; TRANSGENIC MOUSE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL; AXONS; DENDRITES; HUMAN; IMMUNOENZYME TECHNIQUES; MICE; MICE, INBRED C3H; MICE, INBRED C57BL; MICE, TRANSGENIC; MICROSCOPY, ELECTRON; MITOCHONDRIA; MOTOR NEURON DISEASE; MOTOR NEURONS; MUTATION; SUPEROXIDE DISMUTASE; SUPPORT, NON-U.S. GOV'T; SUPPORT, U.S. GOV'T, P.H.S.; VACUOLES;

EID: 0029053881     PISSN: 08966273     EISSN: None     Source Type: Journal    
DOI: 10.1016/0896-6273(95)90259-7     Document Type: Article

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