Polyglutamine expansion as a pathological epitope in huntington’s disease and four dominant cerebellar ataxias

Nature

Volumn 378, Issue 6555, 1995, Pages 403-406

  Trottier, Yvon ^a   Lutz, Yves ^a   Stevanin, Giovanni ^b   Imbert, Georges ^a   Devys, Didier ^a   Cancel, Géraldine ^a,b   Saudou, Frédéric ^a   Weber, Chantal ^a   David, Gilles ^b   Tora, Laszlo ^a   Agid, Yves ^b   Brice, Alexis ^b   Mandel, Jean Louis ^a  

^a CNRS   (France)

^b PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

Author keywords

[No Author keywords available]

Indexed keywords

GLUTAMINE; MONOCLONAL ANTIBODY; MUTANT PROTEIN; POLYGLUTAMIC ACID; PROTEIN;

ARTICLE; AUTOSOMAL DOMINANT INHERITANCE; CEREBELLAR ATAXIA; GENE INSERTION; HUMAN; HUNTINGTON CHOREA; NERVE DEGENERATION; ONSET AGE; PRIORITY JOURNAL; RETINA DEGENERATION;

ADULT; ANTIBODIES, MONOCLONAL; BLOTTING, WESTERN; CELL LINE; CEREBELLAR ATAXIA; DNA-BINDING PROTEINS; FEMALE; GLUTAMINE; HUMAN; HUNTINGTON DISEASE; MALE; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; SUPPORT, NON-U.S. GOV'T; TATA-BOX BINDING PROTEIN; TRANSCRIPTION FACTORS;

EID: 0028972448     PISSN: 00280836     EISSN: None     Source Type: Journal    
DOI: 10.1038/378403a0     Document Type: Article

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