Glyceroltrioleate/glyceroltrierucate therapy in 16 patients with X-chromosomal adrenoleukodystrophy/adrenomyeloneuropathy: Effect on clinical, biochemical and neurophysiological parameters

European Journal of Pediatrics

Volumn 154, Issue 1, 1995, Pages 64-70

  Korenke, G C ^a   Hunneman, D H ^a   Konler, J ^a   Stockler S ^a   Landmark, K ^a   Hanefeld, F ^a  

^a UNIVERSITY OF GÖTTINGEN   (Germany)

Author keywords

Adrenomyeloneuropathy; Peroxisomal disorder; Very long chain fatty acids Therapy; X chromosomal adrenoleukodystrophy

Indexed keywords

ERUCIC ACID; GLYCEROLTRIERUCATE; LONG CHAIN FATTY ACID; TRIOLEIN; UNCLASSIFIED DRUG;

ADDISON DISEASE; ADOLESCENT; ADRENOLEUKODYSTROPHY; ARTICLE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; ELECTROPHYSIOLOGY; HUMAN; MALE; NUCLEAR MAGNETIC RESONANCE IMAGING; ORAL DRUG ADMINISTRATION; PRIORITY JOURNAL; X CHROMOSOME LINKED DISORDER;

ADOLESCENT; ADRENAL CORTEX FUNCTION TESTS; ADRENOLEUKODYSTROPHY; ADULT; AGE OF ONSET; CHILD; CHILD, PRESCHOOL; DEMYELINATING DISEASES; ERUCIC ACIDS; EVOKED POTENTIALS, SOMATOSENSORY; FATTY ACIDS; HUMAN; LEUKOPENIA; MAGNETIC RESONANCE IMAGING; MALE; MIDDLE AGE; NEURAL CONDUCTION; SPINAL NERVES; THROMBOCYTOPENIA; TRIGLYCERIDES; TRIOLEIN; X CHROMOSOME;

EID: 0028952397     PISSN: 03406199     EISSN: 14321076     Source Type: Journal    
DOI: 10.1007/BF01972976     Document Type: Article

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