Neuropathological changes in two lines of mice carrying a transgene for mutant human Cu,Zn SOD, and in mice overexpressing wild type human SOD: a model of familial amyotrophic lateral sclerosis (FALS)

Brain Research

Volumn 676, Issue 1, 1995, Pages 25-40

  Dal Canto, Mauro C ^a   Gurney, Mark E ^a  

^a NORTHWESTERN UNIVERSITY   (United States)

Author keywords

Brainstem; Cu,Zn superoxide dysmutase (SOD); Familial amyotrophic lateral sclerosis; Motor neuron; Peripheral nerve; Spinal cord; Transgenic mice

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BEHAVIOR; BRAIN REGION; BRAIN STEM; CONTROLLED STUDY; HUMAN; HUMAN TISSUE; MOTONEURON; MOUSE; NONHUMAN; PRIORITY JOURNAL; SPINAL CORD; TRANSGENIC MOUSE; ULTRASTRUCTURE;

AGE OF ONSET; AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL; BRAIN; CELL LINE; CELL SURVIVAL; COPPER; DISEASE MODELS, ANIMAL; FAMILY; GENE EXPRESSION; HUMAN; MICE; MICE, TRANSGENIC; MITOCHONDRIA; MUTATION; SPINAL CORD; SUPEROXIDE DISMUTASE; SUPPORT, NON-U.S. GOV'T; SUPPORT, U.S. GOV'T, P.H.S.; ZINC;

EID: 0028933344     PISSN: 00068993     EISSN: None     Source Type: Journal    
DOI: 10.1016/0006-8993(95)00063-V     Document Type: Article

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