Ursodesoxycholic acid: Effect on Xanthomas in Alagille-Watson syndrome

Journal of Pediatric Gastroenterology and Nutrition

Volumn 19, Issue 4, 1994, Pages 476-477

  Krawinkel, M B ^a   Santer, R ^a   Oldigs, H D ^b  

^a UNIVERSITY OF KIEL   (Germany)

^b Municipal Hospitals ^*  (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

URSODEOXYCHOLIC ACID;

ALAGILLE SYNDROME; CASE REPORT; CHOLESTASIS; DRUG EFFECT; HUMAN; HYPERCHOLESTEROLEMIA; LETTER; LIVER DISEASE; MALE; PRIORITY JOURNAL; SCHOOL CHILD; XANTHOMA;

ALAGILLE SYNDROME; CASE REPORT; HUMAN; INFANT; MALE; URSODEOXYCHOLIC ACID; XANTHOMATOSIS;

EID: 0028148305     PISSN: 02772116     EISSN: 15364801     Source Type: Journal    
DOI: 10.1097/00005176-199411000-00022     Document Type: Letter

References (5)

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2. Deprettere A, Portmann B, Mowat AP. Syndromic paucity of the intrahepatic bile ducts: diagnostic difficulty, severe morbidity throughout early childhood. J Pediatr Gastroenterol Nutr 1987;6:865–71.
3. Bojanovski M, Lukermann R, Schulz-Falten J, Sturm E, Burdelski M, Bojanovski D. Parameters of lipoprotein metabolism and cholestasis in healthy and cholestatic infants and children. Prog Lipid Res 1991;30:295–300.
4. Heuman DM, Mills AS, McCall J, Hylemon PB, Pandak WM, Vlahcevic ZR. Conjugates of ursodeoxycholate protect against cholestasis and hepatocellular necrosis caused by more hydrophobic bile salts. Gastroenterology 1991; 100: 203–11.
5. Balistreri WF, A-Kader H, Setchell KDR. Ursodesoxycholic acid (UDCA) therapy in patients with the Alagille syndrome: results of a multicenter pilot trial [Abstract], Pediatr Res 1991;29(suppl):99A.