Cystic fibrosis is treatment with ursodeoxycholic acid of value?

Scandinavian Journal of Gastroenterology

Volumn 29, Issue S204, 1994, Pages 65-67

  Strandvik, B ^a   Lindblad, A ^a  

^a UNIVERSITY OF GOTHENBURG   (Sweden)

Author keywords

Cirrhosis; Cystic fibrosis; Liver disease; Liver function test; Sclerosing cholangitis; Ursodeoxycholic acid

Indexed keywords

URSODEOXYCHOLIC ACID;

ANIMAL; CLINICAL TRIAL; CYSTIC FIBROSIS; GALLBLADDER DISEASE; HUMAN; LIVER DISEASE; LIVER FUNCTION TEST; REVIEW; ARTICLE; BILIARY TRACT DISEASE; CHOLELITHIASIS; LIVER CIRRHOSIS; ORAL DRUG ADMINISTRATION; PRIORITY JOURNAL; SCLEROSING CHOLANGITIS;

ANIMAL; CLINICAL TRIALS; CYSTIC FIBROSIS; GALLBLADDER DISEASES; HUMAN; LIVER DISEASES; LIVER FUNCTION TESTS; SUPPORT, NON-U.S. GOV'T; URSODEOXYCHOLIC ACID;

EID: 0028122016     PISSN: 00365521     EISSN: None     Source Type: Journal    
DOI: 10.3109/00365529409103628     Document Type: Article

References (40)

1. Identification of the cystic fibrosis gene: genetic analysis
2. Identification of the cystic fibrosis gene: cloning and characterization of complementary cDNA
3. Genotype analysis for A F508, G551D and R553X mutations in children and young adults with cystic fibrosis with and without chronic liver disease
4. Hepatic complications of cystic fibrosis
5. Liver and biliary problems in cystic fibrosis
6. Symptomatic hepatic disease in cystic fibrosis: incidence, course, and outcome of portal systemic shunting
7. Liver transplantation in cystic fibrosis
8. Prolonged neonatal jaundice in cystic fibrosis
9. A distinctive type of biliary cirrhosis of the liver associated with cystic fibrosis of the pancreas
10. The pathological changes in the liver in cystic fibrosis of the pancreas
11. Pathology of cystic fibrosis. Review of the literature and comparison with 146 autopsied cases
12. Sclerosing cholangitis in cystic fibrosis
13. The effects of age on alkaline phosphatase and other serologic liver function tests in normal subjects and patients with cystic fibrosis
14. Fasting serum bile acid levels in relation to liver histopathology in cystic fibrosis
15. Gallbladder disease in cystic fibrosis
16. Volume and emptying of the gallbladder in patients with cystic fibrosis
17. Carcinoma of extrahepatic biliary system in an adult with cystic fibrosis
18. Bile salt kinetics in cystic fibrosis: influence of pancreatic enzyme replacement
19. Bile acid kinetics and bile lipid composition in cystic fibrosis
20. Intestinal bile acid malabsorption in cystic fibrosis: a primary mucosal cell defect
21. Minimal bile acid malabsorption and normal bile acid breath tests in cystic fibrosis and acquired pancreatic insufficiency
22. Aspects of bile acid metabolism in cystic fibrosis
23. Bile acid excretion in cystic fibrosis
24. Excretion of bile acids in urine in healthy children and in children with cystic fibrosis
25. Intestinal bile salts in cystic fibrosis
26. Nephrolithiasis in cystic fibrosis
27. Ursodeoxycholic acid dissolution in gallstones in cystic fibrosis
28. Failure of ursodeoxycholic acid to dissolve radiolucent gallstones in patients with cystic fibrosis
29. Evaluation of an oral ursodeoxycholic acid load in the assessment of bile acid malabsorption in cystic fibrosis
30. Ursodeoxycholic acid therapy in cystic fibrosis-associated liver disease: a dose-response study
31. Effects of ursodeoxycholic acid therapy for liver disease associated with cystic fibrosis
32. Effects of ursodeoxycholic acid on liver function in patients with cystic fibrosis and chronic cholestasis
33. Comprehensive study of the biliary bile acid composition of patients with cystic fibrosis and associated liver disease before and after UDCA administration
34. Utilisation de l'acide ursodésoxycholique dans le traitement des complications hépato-biliaires de la mucoviscidose
35. Effects of ursodeoxycholic acid treatment on nutrition and liver function in patients with cystic fibrosis and longstanding cholestasis
36. Scintigraphic documentation of an improvement in hepatobiliary excretory function after treatment with ursodeoxycholic acid in patients with cystic fibrosis and associated liver disease
37. Liver cirrhosis in cystic fibrosis-therapeutic implications and long-term follow-up
38. Long-term study of the effect of ursodeoxycholic acid on liver morphology and liver function in patients with CF
39. An approach for treating the hepatobiliary disease of cystic fibrosis by somatic gene transfer