Treatment of hereditary tyrosinaemia type I by inhibition of 4-hydroxyphenylpyruvate dioxygenase

The Lancet

Volumn 340, Issue 8823, 1992, Pages 813-817

  Lindstedt, S ^a   Holme, E ^a   Lock, E A ^b   Hjalmarson, O ^c   Strandvik, B ^c  

^a SAHLGRENSKA UNIVERSITY HOSPITAL   (Sweden)

^b AKZO NOBEL CENTRAL RESEARCH   (Netherlands)

^c UNIVERSITY OF GOTHENBURG   (Sweden)

Author keywords

[No Author keywords available]

Indexed keywords

4 HYDROXYPHENYLPYRUVATE DIOXYGENASE; ENZYME INHIBITOR; NITISINONE; OXYGENASE; UNCLASSIFIED DRUG;

ARTICLE; CLINICAL ARTICLE; DRUG EFFICACY; ENZYME INHIBITION; GENETIC DISORDER; HUMAN; HUMAN TISSUE; INFANT; LIVER CANCER; LIVER CIRRHOSIS; ORAL DRUG ADMINISTRATION; PRESCHOOL CHILD; PRIORITY JOURNAL; TYROSINEMIA;

4-HYDROXYPHENYLPYRUVATE DIOXYGENASE; ACETOACETATES; ALPHA-FETOPROTEINS; AMINO ACID METABOLISM, INBORN ERRORS; AMINOLEVULINIC ACID; CHILD; CHILD, PRESCHOOL; CYCLOHEXANONES; ERYTHROCYTES; HEPTANOATES; HUMAN; HYDROXYBENZOIC ACIDS; INFANT; KIDNEY TUBULES; LIVER; NITROBENZOATES; PHENYLALANINE; PHOSPHATES; PORPHOBILINOGEN SYNTHASE; PROTEINURIA; SUPPORT, NON-U.S. GOV'T; TYROSINE;

EID: 0026675589     PISSN: 01406736     EISSN: None     Source Type: Journal    
DOI: 10.1016/0140-6736(92)92685-9     Document Type: Article

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