The li-fraumeni syndrome: From clinical epidemiology to molecular genetics

American Journal of Epidemiology

Volumn 135, Issue 2, 1992, Pages 190-199

  Strong, Louise C ^a   Williams, Wick R ^b   Tainsky, Michael A ^a  

^a UNIVERSITY OF TEXAS MD ANDERSON CANCER CENTER   (United States)

^b NONE

Author keywords

Genes; Mutation; Sarcoma

Indexed keywords

ADULT; AGED; AUTOSOMAL DOMINANT INHERITANCE; CANCER EPIDEMIOLOGY; CANCER INCIDENCE; CANCER SUSCEPTIBILITY; CHILDHOOD CANCER; FAMILIAL CANCER; FEMALE; GENE MUTATION; GENETIC ANALYSIS; HUMAN; MAJOR CLINICAL STUDY; MALE; MOLECULAR GENETICS; PENETRANCE; PRIORITY JOURNAL; RELATIVE; REVIEW; SOFT TISSUE SARCOMA; TUMOR SUPPRESSOR GENE;

ADOLESCENT; CANADA; CHI-SQUARE DISTRIBUTION; CHILD; CHILD, PRESCHOOL; DISEASE SUSCEPTIBILITY; FAMILY HEALTH; FEMALE; GENES, P53; HUMAN; INCIDENCE; INFANT; LI-FRAUMENI SYNDROME; MALE; MODELS, GENETIC; RHABDOMYOSARCOMA; SUPPORT, U.S. GOV'T, P.H.S.; UNITED STATES;

EID: 0026578534     PISSN: 00029262     EISSN: None     Source Type: Journal    
DOI: 10.1093/oxfordjournals.aje.a116271     Document Type: Article

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