Biochemical basis of late-onset neurolipidoses

Developmental Neuroscience

Volumn 13, Issue 4-5, 1991, Pages 197-204

  Conzelmann, E ^a   Sandhoff, K ^b  

^a UNIVERSITY OF WÜRZBURG   (Germany)

^b UNIVERSITY OF BONN   (Germany)

Author keywords

Gangliosidosis; Late onset; Lysosomes; Metachromatic leukodystrophy; Neurolipidosis; Residual activity; Storage diseases

Indexed keywords

LYSOSOME ENZYME;

BIOCHEMISTRY; CELL CULTURE; CONFERENCE PAPER; DEGRADATION; ENZYME ACTIVITY; FEEDING; GANGLIOSIDOSIS; KINETICS; LIPIDOSIS; LYSOSOME; LYSOSOME STORAGE DISEASE; METACHROMATIC LEUKODYSTROPHY; PRIORITY JOURNAL; TURNOVER TIME;

ADULT; BRAIN DISEASES, METABOLIC; CELLS, CULTURED; CHILD; ENZYME TESTS; FIBROBLASTS; GLYCOLIPIDS; HUMAN; INFANT; KINETICS; LEUKOCYTES; LIPID METABOLISM, INBORN ERRORS; LYSOSOMES; MODELS, BIOLOGICAL; PHENOTYPE;

EID: 0026410287     PISSN: 03785866     EISSN: 14219859     Source Type: Journal    
DOI: 10.1159/000112160     Document Type: Article

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