Defective acidification of intracellular organelles in cystic fibrosis

Nature

Volumn 352, Issue 6330, 1991, Pages 70-73

  Barasch, Jonathan ^a   Kiss, Brian ^a   Prince, Alice ^a   Saiman, Lisa ^a   Gruenert, Dieter ^b   Ai Awqati, Qais ^a  

^a Department of Neurology and the Taub Institute for Research on Alzheimer's Disease and the Aging Brain   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

GLYCOPROTEIN; LIGAND;

ACIDIFICATION; ARTICLE; CELL ORGANELLE; CYSTIC FIBROSIS; HUMAN; PRIORITY JOURNAL; PSEUDOMONAS; SIALYLATION; SULFATION;

CELL LINE; CHLORIDE CHANNELS; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; GLYCOSYLATION; GOLGI APPARATUS; HUMAN; HYDROGEN-ION CONCENTRATION; LYSOSOMES; MEMBRANE PROTEINS; POTASSIUM; SUPPORT, NON-U.S. GOV'T; SUPPORT, U.S. GOV'T, P.H.S.; TRANSFERRIN;

PSEUDOMONAS;

EID: 0025784535     PISSN: 00280836     EISSN: None     Source Type: Journal    
DOI: 10.1038/352070a0     Document Type: Article

References (36)

1. Quinton, P. M. Nature301, 421-422 (1983).
2. Knowles, M. R. Science 221,1067-1069 (1983)
3. Schoumacher, R. Nature330, 752-754 (1987).
4. Li, M. Nature331, 358-360 (1988).
5. Hwang, T. Science244, 1351-1353 (1989).
6. Boat, T. Am. Rev. resp. Dis.110, 428-441 (1974).
7. Frates, R. C., Kaizu, T. T. & Last, J. A. Pediatr. Res.17, 30-34 (1983).
8. Wesley, A. Forstner, J Pediatr. Res. 17, 65-69 (1983).
9. Scanlin, T. F„ Wang, Y.-M. & Glick, M. C.Pediatr. Res.19, 368-373 (1985).
10. Riordan, J. Science245, 1066-1073 (1989).
11. Barasch, J., Gershon, M. D., Nunez, E. A., Tamlr, H. & Al-Awqati, Q. J. Cell Biol107, 2137-2147 (1988).
12. Mellman, I„ Fuchs, R. & Helenius, A. A. Rev. Biochem.55, 663-700 (1986).
13. Roff, C. F„ Fuchs, R., Mellman, I. & Robbins, A. J Cell Biol.103, 2283-2297 (1986).
14. Anderson, R. G. W. & Pathak, R.Cell40, 635-643 (1985).
15. Griffiths, G., Holflack, B., Simons, K., Mellman, I. & Kornfeld, S. Cell 52, 329-341 (1988).
16. Wagner, J. A. Nature349, 793-796 (1991).
17. Yamashiro, D. J„ Tycko, B., Fluss, S. R. & Maxfield, F. R.Cell37, 789-800 (1984).
18. Al-Awqati, Q. A. Rev. Cell Biol.2,179-199 (1986).
19. Pohlentz, G„ Klein, D„ Schwarzmann, G., Schmitz, D. & Sandhoff, K.Proc. natn. Acad. Sci.85, 7044-7048 (1988).
20. Busam, K. & Decker, K. Eur. J. Biochem. 160, 23-30 (1986).
21. Roseman, S. Meth. Enzym.8, 354-372 (1966).
22. Taatjes, D, Roth, J. Eur. J. Cell Biol.42, 344-350 (1986).
23. Rosner, H„ Wiegandt, H. & Rahmann, H.J. Neurochem.21, 655-665 (1973).
24. Svennerholm L. & Fredman, P. Biochim. Biophys. Acta617, 97-109 (1980).
25. Fishman, P. H. & Brady, R. O. Science 194, 906-915 (1976).
26. Dickson, R, Willingham, M. C. & Pastan, I.J Cell Biol.89, 29-34 (1981).
27. Klausner, R. Proc. natn. Acad. Sci. U.S.A.80, 2263-2266 (1983).
28. Johnson, R. G. & Scarpa, A. J. biol. Chem.254, 3750-3760 (1979).
29. Bae, H. & Verkman, A. S, Nature348, 637-639 (1990).
30. Cheng, S. et al. Cell 63, 827-834 (1990).
31. Paulson, J. C„ Prieels, J.-P., J. biol. Chem.253, 5617-5624 (1978).
32. Green, E. D„ Gruenebaum, J. Proc. natn. Acad. Sci. U.S.A. 81, 5320-5324 (1984).
33. Kriven, H. C., Ginsburg, V. & Roberts, D. Arch. Biochem. Biophys. 260, 493-496 (1988).
34. Fishman, P. H., Moss, J. & Vaughan, M. J. biol. Chem.251, 4490-4494 (1976).
35. White, J., Kleiian, M. & Helenius, A. Q. Rev. Biophys.16, 151-195 (1983).
36. Griffiths, G. & Simons, K. Science234, 438-443 (1986).