Clinical and immune recovery from Omenn syndrome after bone marrow transplantation

The Journal of Pediatrics

Volumn 114, Issue 4 PART 1, 1989, Pages 596-600

  Junker, Anne K ^a   Chan, Ka Wah ^a   Massing, Bonnie G ^a  

^a UNIVERSITY OF BRITISH COLUMBIA   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

B LYMPHOCYTE; BONE MARROW TRANSPLANTATION; CASE REPORT; FEMALE; HUMAN; HYPOGAMMAGLOBULINEMIA; IMMUNE DEFICIENCY; IMMUNOLOGY; IMMUNOREGULATION; INFANT; OMEN SYNDROME; PRIORITY JOURNAL; SYMPTOMATOLOGY; THERAPY;

BONE MARROW TRANSPLANTATION; CASE REPORT; EOSINOPHILIA; FEMALE; HUMAN; IMMUNOLOGIC DEFICIENCY SYNDROMES; INFANT, NEWBORN; RETICULOENDOTHELIOSIS;

EID: 0024597014     PISSN: 00223476     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0022-3476(89)80702-4     Document Type: Article

References (14)

1. Familial reticuloendotheliosis with eosinophilia
2. Omenn syndrome: familial reticuloendothelosis with eosinophilia and combined immunodeficiency
3. Rapidly fatal familial histocytosis associated with eosinophilia and primary immunological deficiency
4. Combined immunodeficiency and reticuloendotheliosis with eosinophilia
5. A lymphoproliferative syndrome, “cutaneous dystrophy” and combined immune deficency with lack of helper T-cell factor
6. The Omenn's syndrome: histological immunohistochemical and ultrastructural evidence for a partial T cell deficiency evolving in an abnormal proliferation of T lymphocytes and S-100+/T-6+ Langerhans-like cells
7. Inbalances in subsets of T lymphocytes in an inbred pediagree with Omenn's syndrome
8. Association of a lymphocyte purine enzyme deficiency (5′ nucleotidase) with combined immunodeficiency
9. Omenn disease: termination in lymphoma
10. Severe combined immune deficiency: treatment by bone marrow transplantation in 15 infants with HLA haploidentical donors
11. Immunologic responses to bacteriophage ΦX174 in immunodefiency disease
12. Histiocytosis X cells and Langerhans cells: enzyme histochemical and immunological similarities
13. Identification by HLA typing of intrauterine-derived maternal T cells in four patients with severe combined immunodeficency
14. Adoptively transferred immunity persists in human marrow graft recipients