The molecular basis of blood coagulation

Cell

Volumn 53, Issue 4, 1988, Pages 505-518

  Furie, Bruce ^a   Furie, Barbara C ^a  

^a TUFTS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BLOOD CLOTTING FACTOR; FIBRINOGEN; VON WILLEBRAND FACTOR;

AMINO ACID SEQUENCE; ANIMAL; BLOOD CLOTTING; GENETICS; HEMOPHILIA A; HUMAN; MOLECULAR GENETICS; NUCLEOTIDE SEQUENCE; PHYSIOLOGY; REVIEW; SEQUENCE HOMOLOGY;

AMINO ACID SEQUENCE; ANIMAL; BASE SEQUENCE; BLOOD COAGULATION; BLOOD COAGULATION FACTORS; FIBRINOGEN; HEMOPHILIA A; HUMAN; MOLECULAR SEQUENCE DATA; SEQUENCE HOMOLOGY, NUCLEIC ACID; SUPPORT, U.S. GOV'T, P.H.S.; VON WILLEBRAND FACTOR;

EID: 0024292694     PISSN: 00928674     EISSN: None     Source Type: Journal    
DOI: 10.1016/0092-8674(88)90567-3     Document Type: Review

References (111)

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6. Structure of pre-pro-von Willebrand factor and its expression in heterologous cells
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12. Characterization of a complementary deoxyribonucleic acid coding for the γ-chain of human fibrinogen
13. Characterization of complementary deoxyribonucleic acid and genomic deoxyribonucleic acid for the beta chain of human fibrinogen
14. Coagulation factors V and VIII and ceruloplasmin constitute a family of structurally related proteins
15. Molecular cloning of the human gene for von Willebrand factor and identification of the transcription initiation site
16. Characterization of the human blood coagulation Factor XII gene
17. Characterization of human blood coagulation Factor XII cDNA
18. Molecular cloning of cDNA for the α-, β-, and γ-chains of rat fibrinogen. A family of coordinately regulated genes
19. Coordinate accumulation of the mRNAs for the α-, β-, and γ-chains of rat fibrinogen following defibrination
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33. Computer-generated models of blood coagulation Factor Xa, Factor IXa, and thrombin based upon structural homology with other serine proteases
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44. Characterization of the bovine prothrombin gene
45. Characterization of a thrombomodulin cDNA reveals structural similarity to the low density lipoprotein receptor
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47. Expression of completely γ-carboxylated recombinant human prothrombin
48. Recognition site directing vitamin K-dependent γ-carboxylation resides on the propeptide of Factor IX
49. Cloning of a cDNA coding for human factor V, a blood coagulation factor homologous to factor VIII and ceruloplasmin
50. Cloning of cDNAs coding for the heavy chain region and connecting region of human Factor V, a blood coagulation factor with four types of internal repeats
51. Evolution and organization of the fibrinogen locus on chromosome 4: gene duplication accompanied by transposition and inversion
52. Vitamin K-dependent carboxylase: control of enzyme activity by the “propeptide” region of Factor X
53. Isolation and characterization of a cDNA coding for human factor IX
54. Characterization of a cDNA coding for human factor X
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56. The Factor IX phospholipid-binding site is required for calcium-dependent activation of Factor IX by Factor XIa
57. Cloning and sequencing of liver cDNA coding for bovine protein C
58. Isolation and sequence of the cDNA for human protein S, a regulator of blood coagulation
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60. Characterization of a complementary deoxyribonucleic acid coding for human and bovine plasminogen
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62. Assembly of the prothrombinase complex
63. Molecular cloning of the cDNA for tissue factor, the cellular receptor for the initiation of the coagulation protease cascade
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66. Chapel Hill: substitution of histidine for arginine at position 145
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69. The propeptide of rat bone γ-carboxyglutamic acid protein shares nomology with other vitamin K-dependent protein precursors
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72. Partial primary structure of bovine plasma fibronectin: three types of internal homology
73. Proteolytic requirements for thrombin activation of anti-hemophilic factor (factor VIII)
74. Differentiation of metal ion-induced transitions of prothrombin fragment 1
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78. Molecular defect of prothrombin Barcelona
79. Effect of propeptide mutations on posttranslational processing of Factor IX: evidence that β-hydroxylation and γ-carboxylation are independent events
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81. Nucleotide sequence of the gene for the γ-chain of human fibrinogen
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83. Hemophilia B (Factor IX Seattle 2) due to a single nucleotide deletion in the gene for Factor IX
84. cDNA sequences for human von Willebrand factor reveal five types of repeated domains and five possible protein sequence polymophisms
85. Gene deletions correlate with the development of alloantibodies in von Willebrand's disease
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88. Metal binding properties of γ-carboxyglutamic acid
89. Isolation of cDNA clones coding for human tissue factor: primary structure of the protein and cDNA
90. Vitamin K dependent modifications of glutamic acid residues in prothrombin
91. β-Hydroxyaspargine in domains homologous to the epidermal growth factor precursor in vitamin K-dependent protein S
92. β-Hydroxyaspartic acid or β-hydroxyasparagine in bovine low density lipoprotein receptor and in bovine thrombomodulin
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94. Vitamin K-dependent carboxylase: development of a peptide substrate
95. Vitamin K-dependent carboxylase: possible role of the substrate “propeptide” as an intracellular recognition site
96. Localization of the metal-induced conformational transition of bovine prothrombin
97. Molecular cloning of a cDNA encoding human antihaemophilic factor
98. A large region of human Factor VIII is dispensable for in vitro procoagulant activity
99. Vitamin K-dependent carboxylation a synthetic peptide based upon the γ-carboxylation recognition site sequence of the prothrombin propeptide is an active substrate for the carboxylase in vitro
100. Full-length von Willebrand factor (vWF) cDNA encodes a highly repetitive protein considerably larger than the mature vWF subunit
101. Expression of variant von Willebrand factor (vWF) cDNA in heterologous cells: requirement of the pro-polypeptide in vWF multimer formation
102. Biosynthesis of von Willebrand protein by human endothelial cells: processing steps and their intracellular localization
103. Immunolocalization of von Willebrand protein in Weibel-Palade bodies of human endothelial cells
104. Divergent fates of von Willebrand factor and its propolypeptide after secretion from endothelial cells
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106. Human thrombomodulin: complete cDNA sequence and chromosome localization of the gene
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109. Nucleotide sequence of the gene for human Factor IX
110. Recurrent mutations in haemophilia A give evidence for CpG mutation hotspots
111. Characterization of five partial deletions of the factor VIII gene