Elastase-like protease and elastolytic activities expressed in cultured dermal fibroblasts derived from lesional skin of patients with pseudoxanthoma elasticum, actinic elastosis, and cutis laxa

Clinica Chimica Acta

Volumn 176, Issue 2, 1988, Pages 219-224

  Schwartz, Elaine ^a   Cruickshank, Frederick A ^a   Lebwohl, Mark G ^a  

^a MOUNT SINAI SCHOOL OF MEDICINE   (United States)

Author keywords

Elastase; Fibroblast; Skin

Indexed keywords

ELASTASE;

ACTINIC ELASTOSIS; CLINICAL ARTICLE; CUTIS LAXA; HUMAN; PRIORITY JOURNAL; PSEUDOXANTHOMA ELASTICUM;

CATIONS, DIVALENT; CELLS, CULTURED; CUTIS LAXA; ELASTIN; FIBROBLASTS; HUMAN; KERATOSIS; OLIGOPEPTIDES; PANCREATIC ELASTASE; PSEUDOXANTHOMA ELASTICUM; SKIN; SUPPORT, U.S. GOV'T, P.H.S.;

EID: 0023718336     PISSN: 00098981     EISSN: None     Source Type: Journal    
DOI: 10.1016/0009-8981(88)90211-2     Document Type: Article

References (14)

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6. Elastases and elastin degradation
7. Elastase-like enzymes in skin fibroblasts and rat aorta smooth muscle cells
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9. Elastase and neutral cathepsin production by human fibroblasts effect of culture conditions on synthesis and secretion
10. On the presence of a metalloproteinase in human skin fibroblasts that degrades the human skin elastic fiber system
11. Characterization and partial purification of a neutral protease from the serum of a patient with autosomal recessive pulmonary emphysema and cutis laxa
12. A new radioactive assay for enzymes with elastolytic activity using reduced tritiated elastin
13. Protein measurement with the folin phenol reagent
14. The synthesis and analytical use of a highly sensitive and convenient substrate of elastase