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European Journal of Pediatrics

Volumn 143, Issue 3, 1985, Pages 203-208

A case of lipogranulomatosis Farber: some clinical and ultrastructural aspects

(5) Burck, U a Moser, H W b Goebel, H H c Gruttner R a Held, K R a

a UNIVERSITY OF HAMBURG (Germany)

b The John F Kennedy Institute ^* (United States)

c JOHANNES GUTENBERG UNIVERSITY (Germany)

Author keywords

Acid ceramidase deficiency; Arthropathy; Farber disease; Hoarseness; Lipogranulomatosis; Ultrastructure

Indexed keywords

ACYLSPHINGOSINE DEACYLASE;

CASE REPORT; DIAGNOSIS; ELECTRON MICROSCOPY; FARBER DISEASE; HISTIOCYTE; HOARSENESS; HUMAN; LYSOSOME DISEASE; PRIORITY JOURNAL; SKIN BIOPSY; SKIN FIBROBLAST; SUBCUTANEOUS NODULE; SUBCUTANEOUS TISSUE; ULTRASTRUCTURE;

ADULT; AMIDOHYDROLASES; FEMALE; GRANULOMA; HOARSENESS; HUMANS; JOINT DISEASES; LIPOMATOSIS; LYMPHOCYTES; SKIN;

EID: 0021983988 PISSN: 03406199 EISSN: 14321076 Source Type: Journal
DOI: 10.1007/BF00442139 Document Type: Article

Times cited : (31)

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