-
1
-
-
0020492939
-
Hypocarnitinaemia in disorders of organic acid metabolism
-
Allan RJ, Hansch DB, Wu HLC 1982 Hypocarnitinaemia in disorders of organic acid metabolism. Lancet 2:500
-
(1982)
Lancet
, vol.2
, pp. 500
-
-
Allan, R.J.1
Hansch, D.B.2
Wu, H.3
-
3
-
-
0017876814
-
Carnitine metabolism in the fasting rat
-
Brass EP, Hoppel CL 1978 Carnitine metabolism in the fasting rat. J Biol Chem 253:2688
-
(1978)
J Biol Chem
, vol.253
, pp. 2688
-
-
Brass, E.P.1
Hoppel, C.L.2
-
4
-
-
0019325901
-
Relationship between acid-soluble carnitine and coenzyme A pools in vivo
-
Brass EP, Hoppel CL 1980 Relationship between acid-soluble carnitine and coenzyme A pools in vivo. Biochem J 190:459
-
(1980)
Biochem J
, vol.190
, pp. 459
-
-
Brass, E.P.1
Hoppel, C.L.2
-
6
-
-
0000577925
-
Secondary carnitine insufficiency in disorders of organic acid metabolism: Modulation of acyl CoA/CoA ratios by L-camitine in vivo
-
Chalmers RA, Roe CR, Tracey BM, Stacey TE, Hoppel CL, Millington DS 1983 Secondary carnitine insufficiency in disorders of organic acid metabolism: modulation of acyl CoA/CoA ratios by L-camitine in vivo. Biochem Soc Trans 11:724
-
(1983)
Biochem Soc Trans
, vol.11
, pp. 724
-
-
Chalmers, R.A.1
Roe, C.R.2
Tracey, B.M.3
Stacey, T.E.4
Hoppel, C.L.5
Millington, D.S.6
-
7
-
-
0021226458
-
L-Carnitine insufficiency in disorders of organic acid metabolism: Response to L-carnitine by patients with methylmalonic aciduria and 3-hydroxy-3-methylglutaric aciduria
-
Chalmers RA, Stacey TE, Tracey BM, de Sousa C, Roe CR, Millington DS, Hoppel CL 1984 L-Carnitine insufficiency in disorders of organic acid metabolism: response to L-carnitine by patients with methylmalonic aciduria and 3-hydroxy-3-methylglutaric aciduria. J Inherited Metab Dis (Suppl. 2): 109
-
(1984)
J Inherited Metab Dis (Suppl
, vol.2
, pp. 109
-
-
Chalmers, R.A.1
Stacey, T.E.2
Tracey, B.M.3
De Sousa, C.4
Roe, C.R.5
Millington, D.S.6
Hoppel, C.L.7
-
8
-
-
0014117707
-
PH-dependence of carnitine acetyltransferase activity
-
Chase JFA 1967 pH-dependence of carnitine acetyltransferase activity. Biochem J 104:503
-
(1967)
Biochem J
, vol.104
, pp. 503
-
-
Chase, J.1
-
9
-
-
0014117259
-
The substrate specificity of carnitine acetyltransferase
-
Chase JFA 1967 The substrate specificity of carnitine acetyltransferase. Biochem J 104:510
-
(1967)
Biochem J
, vol.104
, pp. 510
-
-
Chase, J.1
-
10
-
-
0013894041
-
Some kinetic studies on the mechanism of action of carnitine acetyltransferase
-
Chase JFA, Tubbs PK 1966 Some kinetic studies on the mechanism of action of carnitine acetyltransferase. Biochem J 99:32
-
(1966)
Biochem J
, vol.99
, pp. 32
-
-
Chase, J.1
Tubbs, P.K.2
-
11
-
-
0020001119
-
C6-C0 diarboxylic aciduria: Investigations of a patient with riboflavin responsive multiple acyl CoA dehydrogenase defects
-
Gregersen N, Wintzensen H, Kplvraa S, Christensen E, Christensen, HF, Brandt NJ, Rasmussen K 1982 C6-C0 diarboxylic aciduria: investigations of a patient with riboflavin responsive multiple acyl CoA dehydrogenase defects. Pediatr Res 16:861
-
(1982)
Pediatr Res
, vol.16
, pp. 861
-
-
Gregersen, N.1
Wintzensen, H.2
Kplvraa, S.3
Christensen, E.4
Christensen, H.F.5
Brandt, N.J.6
Rasmussen, K.7
-
12
-
-
0020173087
-
Urinary excretion of acetylcamitine during human diabetic and fasting ketosis
-
Hoppel CL, Genuth SM 1982 Urinary excretion of acetylcamitine during human diabetic and fasting ketosis. Am J Physiol 243:168
-
(1982)
Am J Physiol
, vol.243
, pp. 168
-
-
Hoppel, C.L.1
Genuth, S.M.2
-
13
-
-
0015595662
-
The effect of acute and prolonged ethanol treatment on the contents of coenzyme A, carnitine and their derivatives in rat liver
-
Kondrup J, Grunnet N 1973 The effect of acute and prolonged ethanol treatment on the contents of coenzyme A, carnitine and their derivatives in rat liver. Biochem J 132:373
-
(1973)
Biochem J
, vol.132
, pp. 373
-
-
Kondrup, J.1
Grunnet, N.2
-
14
-
-
0019310364
-
Tissue distribution of carnitine biosynthetic enzymes in man
-
Rebouche CJ, Engel AG 1980 Tissue distribution of carnitine biosynthetic enzymes in man. Biochim Biophys Acta 630:22
-
(1980)
Biochim Biophys Acta
, vol.630
, pp. 22
-
-
Rebouche, C.J.1
Engel, A.G.2
-
15
-
-
0020069722
-
L-Carnitine therapy in propionic acidaemia
-
Roe CR, Bohun TP 1982 L-Carnitine therapy in propionic acidaemia. Lancet 1:1411
-
(1982)
Lancet
, vol.1
, pp. 1411
-
-
Roe, C.R.1
Bohun, T.P.2
-
16
-
-
0021028824
-
Metabolic response to carnitine in methylmalonic aciduria: An effective strategy for elimination of propionyl groups
-
Roe CR, Hoppel CL, Stacey TE, Chalmers RA, Tracey BM, Millington DS 1983 Metabolic response to carnitine in methylmalonic aciduria: an effective strategy for elimination of propionyl groups. Arch Dis Child 58:916
-
(1983)
Arch Dis Child
, vol.58
, pp. 916
-
-
Roe, C.R.1
Hoppel, C.L.2
Stacey, T.E.3
Chalmers, R.A.4
Tracey, B.M.5
Millington, D.S.6
-
17
-
-
0021238320
-
L-Camitine enhances excretion of propionyl CoA as propionylcarnitine in propionic acidemia
-
Roe CR, Millington DS, Hoppel CL, Maltby DA, Bohun TP 1984 L-Camitine enhances excretion of propionyl CoA as propionylcarnitine in propionic acidemia. J Clin Invest 73:1785
-
(1984)
J Clin Invest
, vol.73
, pp. 1785
-
-
Roe, C.R.1
Millington, D.S.2
Hoppel, C.L.3
Maltby, D.A.4
Bohun, T.P.5
|