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Volumn 18, Issue 12, 1984, Pages 1325-1328

Urinary excretion of l-carnitine and acylcarnitines by patients with disorders of organic acid metabolism: Evidence for secondary insufficiency of l-carnitine

Author keywords

[No Author keywords available]

Indexed keywords

ACYLCARNITINE; CARNITINE;

EID: 0021710439     PISSN: 00313998     EISSN: 15300447     Source Type: Journal    
DOI: 10.1203/00006450-198412000-00021     Document Type: Article
Times cited : (213)

References (18)
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    • Secondary carnitine insufficiency in disorders of organic acid metabolism: Modulation of acyl CoA/CoA ratios by L-camitine in vivo
    • Chalmers RA, Roe CR, Tracey BM, Stacey TE, Hoppel CL, Millington DS 1983 Secondary carnitine insufficiency in disorders of organic acid metabolism: modulation of acyl CoA/CoA ratios by L-camitine in vivo. Biochem Soc Trans 11:724
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    • Chalmers, R.A.1    Roe, C.R.2    Tracey, B.M.3    Stacey, T.E.4    Hoppel, C.L.5    Millington, D.S.6
  • 7
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    • Chalmers RA, Stacey TE, Tracey BM, de Sousa C, Roe CR, Millington DS, Hoppel CL 1984 L-Carnitine insufficiency in disorders of organic acid metabolism: response to L-carnitine by patients with methylmalonic aciduria and 3-hydroxy-3-methylglutaric aciduria. J Inherited Metab Dis (Suppl. 2): 109
    • (1984) J Inherited Metab Dis (Suppl , vol.2 , pp. 109
    • Chalmers, R.A.1    Stacey, T.E.2    Tracey, B.M.3    De Sousa, C.4    Roe, C.R.5    Millington, D.S.6    Hoppel, C.L.7
  • 8
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    • Chase, J.1
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    • The substrate specificity of carnitine acetyltransferase
    • Chase JFA 1967 The substrate specificity of carnitine acetyltransferase. Biochem J 104:510
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    • Chase, J.1
  • 10
    • 0013894041 scopus 로고
    • Some kinetic studies on the mechanism of action of carnitine acetyltransferase
    • Chase JFA, Tubbs PK 1966 Some kinetic studies on the mechanism of action of carnitine acetyltransferase. Biochem J 99:32
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    • Urinary excretion of acetylcamitine during human diabetic and fasting ketosis
    • Hoppel CL, Genuth SM 1982 Urinary excretion of acetylcamitine during human diabetic and fasting ketosis. Am J Physiol 243:168
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    • Hoppel, C.L.1    Genuth, S.M.2
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    • The effect of acute and prolonged ethanol treatment on the contents of coenzyme A, carnitine and their derivatives in rat liver
    • Kondrup J, Grunnet N 1973 The effect of acute and prolonged ethanol treatment on the contents of coenzyme A, carnitine and their derivatives in rat liver. Biochem J 132:373
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    • Roe, C.R.1    Hoppel, C.L.2    Stacey, T.E.3    Chalmers, R.A.4    Tracey, B.M.5    Millington, D.S.6
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* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.