The proteus syndrome - Partial gigantism of the hands and/or feet, nevi, hemihypertrophy, subcutaneous tumors, macrocephaly or other skull anomalies and possible accelerated growth and visceral affections

European Journal of Pediatrics

Volumn 140, Issue 1, 1983, Pages 5-12

  Wiedemann, H R ^a   Burgio, G R ^b   Aldenhoff, P ^c   Kunze, J ^c   Kaufmann, H J ^c   Schirg, E ^d  

^a UNIVERSITY HOSPITAL SCHLESWIG HOLSTEIN   (Germany)

^b FONDAZIONE IRCCS POLICLINICO SAN MATTEO   (Italy)

^c FREIE UNIVERSITÄT BERLIN   (Germany)

^d Institute of Cellular Biochemistry   (Germany)

Author keywords

Hemihypertrophy; Lipomas; Macrodactyly; Pigmented nevi; Proteus syndrome; Skull anomalies

Indexed keywords

BONE; CENTRAL NERVOUS SYSTEM; CHILD; CONGENITAL DISORDER; ETIOLOGY; FOOT; GIGANTISM; GROWTH ACCELERATION; GROWTH DISORDER; HAMARTOMA; HAND; HEMIHYPERTROPHY; HUMAN; INHERITANCE; LIPOMA; MACROCEPHALY; MACRODACTYLY; MAJOR CLINICAL STUDY; METHODOLOGY; MUSCULOSKELETAL SYSTEM; NEVUS; SKULL MALFORMATION; SUBCUTANEOUS TISSUE;

ABNORMALITIES, MULTIPLE; CHILD; CHILD, PRESCHOOL; FOOT DEFORMITIES, CONGENITAL; HAND DEFORMITIES, CONGENITAL; HUMANS; LUNG; MALE; NEVUS, PIGMENTED; SKIN NEOPLASMS; SKULL; SYNDROME;

EID: 0020534650     PISSN: 03406199     EISSN: 14321076     Source Type: Journal    
DOI: 10.1007/BF00661895     Document Type: Article

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