The Sickle Cell Diseases: Clinical Manifestations Including the Sickle Crisis

Archives of Internal Medicine

Volumn 133, Issue 4, 1974, Pages 611-619

  Konotey Ahulu, Felix I D ^a  

^a KORLE BU TEACHING HOSPITAL   (Ghana)

Author keywords

[No Author keywords available]

Indexed keywords

CLASSIFICATION; ETIOLOGY; PEDIATRICS; PREVENTION; REVIEW; SICKLE CELL ANEMIA; SICKLE CELL CRISIS;

ADULT; ANEMIA, HEMOLYTIC; ANEMIA, SICKLE CELL; CHILD; CHILD, PRESCHOOL; COMPREHENSIVE HEALTH CARE; FEMALE; FOOT DISEASES; GENOTYPE; GHANA; GLUCOSEPHOSPHATE DEHYDROGENASE DEFICIENCY; GROWTH DISORDERS; HAND; HEMATURIA; HUMAN; INFANT; MALE; NEGROID RACE; PAIN; PALLOR; PHENOTYPE; PUBLIC HEALTH; SOCIOECONOMIC FACTORS; TERMINOLOGY;

EID: 0016188324     PISSN: 00039926     EISSN: 15383679     Source Type: Journal    
DOI: 10.1001/archinte.1974.00320160105009     Document Type: Article

References (41)

1. Herrick JB: Peculiar elongated and sickle shaped red blood corpuscles in a case of severe anaemia. Arch Intern Med 6:517-521, 1910.
2. Konotey-Ahulu FID: Hereditary qualitative and quantitative erythrocyte defects in Ghana: An historical and geographical survey. Ghana Med J 7:118-119, 1968.
3. Konotey-Ahulu FID: Sickle-cell disease in successive Ghanaian generations for three centuries, in Sickle-cell Disease: Natural History From a Clinico-Epidemiological Study of 1,550 Consecutive Patients. Ghana, Ghana University Press, to be published.
4. Konotey-Ahulu FID: Computer assisted analysis of data on 1,697 patients attending the sickle cell/haemoglobinopathy clinic of Korle Bu Teaching Hospital, Accra, Ghana: Clinical features: I. Sex, genotype, age, rheumatism and dactylitis frequencies. Ghana Med J 10:241-260, 1971.
5. Lehmann H, Huntsman RC: Man's Haemoglobin. Amsterdam, North Holland Publishing Co, 1966.
6. Ringelhann B, Khorsandi M: Hemoglobin crystallization test to differentiate cells with Hb SC and CC genotype from SS cells without electrophoresis. Am J Clin Pathol 57:467-470, 1972.
7. WHO Scientific Group on the standardization of procedures for the study of glucose-6-phosphatedehydrogenase. WHO Tech Rep Ser 366:1-53, 1967.
8. Ringelhann B: A simple laboratory procedure for the recognition of A (African type) G 6PD deficiency in acute haemolytic crisis. Clin Chim Acta 36:272-274, 1972.
9. Woodruff AW, et al: Terminology of the hereditary haemoglobinopathies with haemoglobin variants. Br Med J 1:1235, 1957.
10. WHO Scientific Group Report: Hemoglobinopathies and allied disorders. WHO Tech Rep Ser 338:1-40, 1966.
11. Konotey-Ahulu FID: Definition of sickle trait and sickle cell disease. Ghana Med J 11:417-420,1972.
12. Konotey-Ahulu FID: Sickle-cell trait and altitude. Br Med J 1:177-178, 1972.
13. Konotey-Ahulu FID: Sickle cell and altitude. Br Med J 2:231, 1972.
14. Addae RO: Sickle cell trait and altitude. Br Med J 1:53, 1972.
15. Konotey-Ahulu FID: Balanced polymorphism and hereditary qualitative and quantitative erythrocyte defects. Ghana Med J 11:274-285, 1972.
16. Konotey-Ahulu FID: Malaria and sickle cell disease. Br Med J 2:710-711, 1971.
17. Konotey-Ahulu FID: Treatment and prevention of sickle-cell crisis. Lancet 2:1255, 1971.
18. Konotey-Ahulu FID: Sicklaemic human hygrometers. Lancet 1:1003-1004, 1965.
19. Konotey-Ahulu FID: Management of patients with sickle-cell disease. Lancet 2:772, 1972.
20. Diggs LW: Sickle-cell crises. Am J Clin Pathol 44:1-19, 1965.
21. Fullerton WT, Watson-Williams EJ: Haemoglobin SC disease and megaloblastic anaemia of pregnancy. J Obstet Gynaecol Br Commonw 69:729-735, 1962.
22. Fullerton WT, Hendrickse JP de V, Watson-Williams EJ: Haemoglobin SC disease in pregnancy: A review of 190 cases, in Jonxis JHP (ed): Abnormal Haemoglobins in Africa. Oxford, England, Blackwell Scientific Publications, 1965, pp 411-433.
23. Watson-Williams EJ: The management of patients with abnormal haemoglobin disorders in pregnancy, in Maegraith BG, Gilles HM (eds): Management and Treatment of Tropical Diseases. Oxford, England, Blackwell Scientific Publications, 1971, pp 56-58.
24. Konotey-Ahulu FID: Sickle cell Disease: The Case for Family Planning. Accra, Ghana, Astab Books Ltd, 1973, p 11.
25. Konotey-Ahulu FID: The pathogenesis of sickle-cell crisis in Ghana. Ghana Med J 11:304-306, 1972.
26. Addae S: Mechanism for the high incidence of sickle-cell crisis in the tropical cool season. Lancet 2:1256, 1971.
27. Addae SK: Aspects of renal function in sicklecell crisis. Ghana Med J 11:242-247, 1972.
28. Addae SK: The Effect of Different Ambient Temperatures on Some Renal Functions in Sickle Cell Haemoglobinopathy, thesis. London, 1972.
29. Lowe RC, Adams CC: Studies on the pathophysiology of sickle-cell disease. Ann Intern Med 22:192-200, 1945.
30. Grover V: Clinical manifestations of sickle-cell anaemia. Ann Intern Med J 26:843-851, 1947.
31. Konotey-Ahulu FID: Epistaxis in sickle-cell anaemia. Br Med J 1:234, 1966.
32. Konotey-Ahulu FID: Patterns of clinical haemoglobinopathy. East Afr Med J 46:149-156, 1949.
33. Konotey-Ahulu FID: Mental-nerve neuropathy: A complication of sickle-cell crisis. Lancet 2:388, 1972.
34. Konotey-Ahulu FID: Effect of environment on sickle cell disease in West Africa: Epidemiologic and clinical considerations, in Abramson H, Bertles JF, Wethers D (eds): Symposium on Sickle-Cell Disease: Diagnosis, Management, Education and Research. St Louis, CV Mosby Co, 1973, pp 20-38.
35. Konotey-Ahulu FID: The liver in sickle-cell disease: Clinical aspects. Ghana Med J 8:104-118, 1969.
36. Serjeant GR: The clinical features in adults with sickle-cell anaemia in Jamaica. West Ind Med J 19:1-8, 1970.
37. Konotey-Ahulu FID, Kuma E: Skeletal crumbling in sickle cell anaemia complicated by Salmonella typhi infection. Br J Clin Pract 19:575-578, 1965.
38. Konotey-Ahulu FID: Hip disease in Africans. Lancet 1:999, 1970.
39. Konotey-Ahulu FID, Ringelhann B: Sickle-cell anaemia, sickle-cell thalassaemia, sickle-cell haemoglobin C disease and asymptomatic haemoglobin C thalassaemia in one Ghanaian family. Br Med J 1:607-612, 1969.
40. Ringelhann B, Konotey-Ahulu FID: Immunological studies in sickle cell crisis in Ghana. Afr J Med Sci 4:17-22, 1973.
41. WHO Scientific Group Report: Treatment of haemoglobinopathies and allied disorders. WHO Tech Rep Ser 509:1-83, 1972.